A tapetoretinal degeneration with symmetrical calcifications of the basal ganglia. A hereditary disease.

Tapetoretinal degeneration in 3 members of a family is documented with fundus photographs and fluorescein angiograms. Computer tomograms showed intracranial symmetrical calcifications of the central nervous system in 2 patients. Laboratory examinations also indicated a disturbance in calcium metabolism. An autosomal dominant mode of inheritance is probably present.