Atrial septal defect associated with drainage of left superior vena cava to left atrium and absence of the coronary sinus.

Atrial septal defect associated with drainage of the left superior vena cava (LSVC) to the left atrium and absence of the coronary sinus is a rare congenital cardiac complex. Management of the LSVC during operative repair is usuall by one of three methods: (1) an intra-atrial baffle of pericardium to divery flow from the LSVC to the right arrium and to close the atrial septal defect; (2) division and reimplantation of the LSVC into the right atrium; or (3) simple ligation of the LSVC. We will present an example of this cardiac lesion for which successful repair was achieved by end-to-side anastomosis of the LSVC to the main pulmonary artery when none of the aforementioned methods for handling the LSVC was feasible.