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115 in total

1. An alpha-subunit loop structure is required for GM2 activator protein binding by beta-hexosaminidase A.

Authors: Maryam Zarghooni; Scott Bukovac; Michael Tropak; John Callahan; Don Mahuran
Journal: Biochem Biophys Res Commun Date: 2004-11-19 Impact factor: 3.575

2. Expression and routeing of human lysosomal alpha-glucosidase in transiently transfected mammalian cells.

Authors: L H Hoefsloot; R Willemsen; M A Kroos; M Hoogeveen-Westerveld; M M Hermans; A T Van der Ploeg; B A Oostra; A J Reuser
Journal: Biochem J Date: 1990-12-01 Impact factor: 3.857

Review 3. Human biochemical genetics of enzyme proteins in the new age of molecular genetics.

Authors: D M Swallow; D A Hopkinson
Journal: J Inherit Metab Dis Date: 1986 Impact factor: 4.982

Review 4. The early and late processing of lysosomal enzymes: proteolysis and compartmentation.

Authors: A Hasilik
Journal: Experientia Date: 1992-02-15

5. A quantitative immunoelectronmicroscopic study on soluble, membrane-associated and membrane-bound lysosomal enzymes in human intestinal epithelial cells.

Authors: R Willemsen; R Brünken; C W Sorber; A T Hoogeveen; H A Wisselaar; J M Van Dongen; A J Reuser
Journal: Histochem J Date: 1991-10

6. Heterogeneity of pig lysosomal acid alpha-glucosidase. Affinity to Sephacryl S-200 gel and tissue distribution.

Authors: S Nakasone; T Ohshita; T Iwamasa
Journal: Biochem J Date: 1991-11-01 Impact factor: 3.857

7. Identification of a variant of mucolipidosis III (pseudo-Hurler polydystrophy): a catalytically active N-acetylglucosaminylphosphotransferase that fails to phosphorylate lysosomal enzymes.

Authors: A P Varki; M L Reitman; S Kornfeld
Journal: Proc Natl Acad Sci U S A Date: 1981-12 Impact factor: 11.205

8. Synthesis of beta-hexosaminidase in cell-free translation and in intact fibroblasts: an insoluble precursor alpha chain in a rare form of Tay-Sachs disease.

Authors: R L Proia; E F Neufeld
Journal: Proc Natl Acad Sci U S A Date: 1982-10 Impact factor: 11.205

9. Cellular uptake of saposin (SAP) precursor and lysosomal delivery by the low density lipoprotein receptor-related protein (LRP).

Authors: T Hiesberger; S Hüttler; A Rohlmann; W Schneider; K Sandhoff; J Herz
Journal: EMBO J Date: 1998-08-17 Impact factor: 11.598

10. alpha-L-iduronidase therapy for mucopolysaccharidosis type I.

Authors: Jakub Tolar; Paul J Orchard
Journal: Biologics Date: 2008-12