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203 in total

1. Role of beta Arg211 in the active site of human beta-hexosaminidase B.

Authors: Y Hou; D Vocadlo; S Withers; D Mahuran
Journal: Biochemistry Date: 2000-05-23 Impact factor: 3.162

2. Proteolytic processing and glycosylation of cathepsin B. The role of the primary structure of the latent precursor and of the carbohydrate moiety for cell-type-specific molecular forms of the enzyme.

Authors: L Mach; K Stüwe; A Hagen; C Ballaun; J Glössl
Journal: Biochem J Date: 1992-03-01 Impact factor: 3.857

3. Post-translational modifications of the gamma-subunit affect intracellular trafficking and complex assembly of GlcNAc-1-phosphotransferase.

Authors: Marisa Encarnação; Katrin Kollmann; Maria Trusch; Thomas Braulke; Sandra Pohl
Journal: J Biol Chem Date: 2010-12-20 Impact factor: 5.157

4. Nucleotide sequence of cloned cDNA for human sphingolipid activator protein 1 precursor.

Authors: N N Dewji; D A Wenger; J S O'Brien
Journal: Proc Natl Acad Sci U S A Date: 1987-12 Impact factor: 11.205

5. Biosynthesis, processing, and extracellular release of alpha-L-fucosidase in lymphoid cell lines of different genetic origins.

Authors: R A DiCioccio; K S Brown
Journal: Biochem Genet Date: 1988-06 Impact factor: 1.890

6. Regional mapping of the human gene for lysosomal alpha-glucosidase by in situ hybridization.

Authors: D J Halley; A Konings; P Hupkes; H Galjaard
Journal: Hum Genet Date: 1984 Impact factor: 4.132

7. Identification of a variant of mucolipidosis III (pseudo-Hurler polydystrophy): a catalytically active N-acetylglucosaminylphosphotransferase that fails to phosphorylate lysosomal enzymes.

Authors: A P Varki; M L Reitman; S Kornfeld
Journal: Proc Natl Acad Sci U S A Date: 1981-12 Impact factor: 11.205

8. Mutations of glucocerebrosidase: discrimination of neurologic and non-neurologic phenotypes of Gaucher disease.

Authors: E I Ginns; R O Brady; S Pirruccello; C Moore; S Sorrell; F S Furbish; G J Murray; J Tager; J A Barranger
Journal: Proc Natl Acad Sci U S A Date: 1982-09 Impact factor: 11.205

9. Synthesis of beta-hexosaminidase in cell-free translation and in intact fibroblasts: an insoluble precursor alpha chain in a rare form of Tay-Sachs disease.

Authors: R L Proia; E F Neufeld
Journal: Proc Natl Acad Sci U S A Date: 1982-10 Impact factor: 11.205

Review 10. Review: the immunochemical analysis of enzyme from mucopolysaccharidoses patients.

Authors: D A Brooks
Journal: J Inherit Metab Dis Date: 1993 Impact factor: 4.982