Papillary-cystic carcinoma of the pancreas.

Papillary-cystic carcinoma of the pancreas is an extremely rare tumor which occurs in young adults, may invade locally, but is late to metastasize. As opposed to adenocarcinoma of the pancreas, portal vein invasion should not be included as a criteria for nonresectability. In the absence of metastatic disease, pancreatectomy combined with portal vein resection, if invasion is present, may offer a good prognosis and comparatively long survival time.