Literature DB >> 668142

Lipoamide dehydrogenase in cultured human skin fibroblasts.

S B Melançon, L Dallaire, M Potier.   

Abstract

Lipoamide dehydrogenase was identified in cultured skin fibroblasts of normal individuals and patients with Friedreich's ataxia. The optimum conditions for its assay were defined. Data disclosed a normal range of 36--122 mumol/min/mg protein in control fibroblasts and 61--112 mumol/min/mg protein in patients fibroblasts. Numerous precautions should be taken in handling fibroblast cultures for lipoamide dehydrogenase determination.

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Year:  1978        PMID： 668142     DOI： 10.1016/0009-8981(78)90053-0

Source DB:  PubMed          Journal:  Clin Chim Acta        ISSN： 0009-8981            Impact factor:   3.786


  2 in total

1.  Lactic acidemia, neurologic deterioration and carbohydrate dependence in a girl with dihydrolipoyl dehydrogenase deficiency.

Authors:  B H Robinson; J Taylor; S G Kahler; H N Kirkman
Journal:  Eur J Pediatr       Date:  1981-03       Impact factor: 3.183

2.  A familial progressive neurodegenerative disease with 2-oxoglutaric aciduria.

Authors:  A Kohlschütter; A Behbehani; U Langenbeck; M Albani; P Heidemann; G Hoffmann; J Kleineke; W Lehnert; U Wendel
Journal:  Eur J Pediatr       Date:  1982-02       Impact factor: 3.183
  2 in total

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