Literature DB >> 6622965

High excretion of beta-aminoisobutyric acid in patients with ketoacidosis.

S Landaas, E Solem.   

Abstract

High concentrations of beta-aminoisobutyric acid (BAIBA) were found to be present in the urine from patients with ketoacidosis. The R-form was always the dominating isomer of BAIBA. The finding is discussed, and it is suggested that the mechanism might be a derangement in the degradation of valine.

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Year:  1983        PMID： 6622965

Source DB:  PubMed          Journal:  Scand J Clin Lab Invest        ISSN： 0036-5513            Impact factor:   1.713


  4 in total

1.  Gaussian and linear deconvolution of LC-MS/MS chromatograms of the eight aminobutyric acid isomers.

Authors:  Harika Vemula; Yukiko Kitase; Navid J Ayon; Lynda Bonewald; William G Gutheil
Journal:  Anal Biochem       Date:  2016-10-19       Impact factor: 3.365

2.  New insights in dihydropyrimidine dehydrogenase deficiency: a pivotal role for beta-aminoisobutyric acid?

Authors:  André B P Van Kuilenburg; Alida E M Stroomer; Henk Van Lenthe; Nico G G M Abeling; Albert H Van Gennip
Journal:  Biochem J       Date:  2004-04-01       Impact factor: 3.857

3.  Excessive excretion of beta-alanine and of 3-hydroxypropionic, R- and S-3-aminoisobutyric, R- and S-3-hydroxyisobutyric and S-2-(hydroxymethyl)butyric acids probably due to a defect in the metabolism of the corresponding malonic semialdehydes.

Authors:  R J Pollitt; A Green; R Smith
Journal:  J Inherit Metab Dis       Date:  1985       Impact factor: 4.982

4.  Severe child form of primary hyperoxaluria type 2 - a case report revealing consequence of GRHPR deficiency on metabolism.

Authors:  Jana Konkoľová; Ján Chandoga; Juraj Kováčik; Marcel Repiský; Veronika Kramarová; Ivana Paučinová; Daniel Böhmer
Journal:  BMC Med Genet       Date:  2017-05-31       Impact factor: 2.103
  4 in total

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