Surgical management of absent right pulmonary artery with associated pulmonary hypertension.

A critically ill 21-month-old girl with congenital absence of the right pulmonary artery and severe pulmonary hypertension and congestive heart failure underwent conduit restoration of flow to the right lung. This patient had marked clinical improvement and reduction in pulmonary hypertension and represents the second reported surgically-treated case for absent right pulmonary artery. Reestablishment of pulmonary artery continuity is therefore recommended when cardiac failure and pulmonary hypertension occurs.