Literature DB >> 6568950

Functional deficiency of complement factor D in a monozygous twin.

H C Kluin-Nelemans, H van Velzen-Blad, H P van Helden, M R Daha.   

Abstract

An adult twin with recurrent bacterial infections was found to have a partial functional deficiency of complement factor D. Full restoration of alternative pathway activity and zymosan- or cobra venom factor-induced consumption of C3 and B was found after reconstitution of patient's serum with purified D. Family studies revealed normal D levels in the mother, a brother and another sister. After gel filtration of patient's sera only little D activity could be detected in the fractions, and trypsin activation of the fractions also did not uncover detectable precursor D activity.

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Year:  1984        PMID: 6568950      PMCID: PMC1577100     

Source DB:  PubMed          Journal:  Clin Exp Immunol        ISSN: 0009-9104            Impact factor:   4.330


  18 in total

Review 1.  Complement deficiency states.

Authors:  V Agnello
Journal:  Medicine (Baltimore)       Date:  1978-01       Impact factor: 1.889

Review 2.  Genetic polymorphism of human complement proteins.

Authors:  G Hauptmann
Journal:  Rev Fr Transfus Immunohematol       Date:  1979-12

Review 3.  Role of complement in the induction of immunological responses.

Authors:  M B Pepys
Journal:  Transplant Rev       Date:  1976

4.  Hypocomplementaemia due to a genetic deficiency of beta 1H globulin.

Authors:  R A Thompson; M H Winterborn
Journal:  Clin Exp Immunol       Date:  1981-10       Impact factor: 4.330

5.  C3b inactivator deficiency with immune complex manifestations.

Authors:  P Solal-Celigny; M Laviolette; J Hebert; P C Atkins; M Sirois; G Brun; G Lehner-Netsch; J M Delâge
Journal:  Clin Exp Immunol       Date:  1982-01       Impact factor: 4.330

6.  Enhanced alternative complement pathway-dependent degradation of soluble immunoglobulin aggregates by macrophages.

Authors:  M R Daha; L A Van Es
Journal:  Immunology       Date:  1981-07       Impact factor: 7.397

7.  C3 nephritic factor (C3NeF): stabilization of fluid phase and cell-bound alternative pathway convertase.

Authors:  M R Daha; D T Fearon; K F Austen
Journal:  J Immunol       Date:  1976-01       Impact factor: 5.422

8.  Inhibition of secondary in vitro antibody responses by the third component of complement.

Authors:  M V Hobbs; T L Feldbush; B W Needleman; J M Weiler
Journal:  J Immunol       Date:  1982-03       Impact factor: 5.422

9.  The activation of the alternative pathway C3 convertase by human plasma kallikrein.

Authors:  R G DiScipio
Journal:  Immunology       Date:  1982-03       Impact factor: 7.397

10.  Familial partial deficiency of the third component of complement (C3) and the hypocomplementemic cutaneous vasculitis syndrome.

Authors:  R H McLean; A Weinstein; J Chapitis; M Lowenstein; N F Rothfield
Journal:  Am J Med       Date:  1980-04       Impact factor: 4.965

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  8 in total

Review 1.  Complement deficiency.

Authors:  K M O'Neil
Journal:  Clin Rev Allergy Immunol       Date:  2000-10       Impact factor: 8.667

2.  A family with complement factor D deficiency.

Authors:  D H Biesma; A J Hannema; H van Velzen-Blad; L Mulder; R van Zwieten; I Kluijt; D Roos
Journal:  J Clin Invest       Date:  2001-07       Impact factor: 14.808

Review 3.  Infectious diseases associated with complement deficiencies.

Authors:  J E Figueroa; P Densen
Journal:  Clin Microbiol Rev       Date:  1991-07       Impact factor: 26.132

4.  Complete and partial deficiencies of complement factor D in a Dutch family.

Authors:  P S Hiemstra; E Langeler; B Compier; Y Keepers; P C Leijh; M T van den Barselaar; D Overbosch; M R Daha
Journal:  J Clin Invest       Date:  1989-12       Impact factor: 14.808

5.  Small-molecule factor D inhibitors selectively block the alternative pathway of complement in paroxysmal nocturnal hemoglobinuria and atypical hemolytic uremic syndrome.

Authors:  Xuan Yuan; Eleni Gavriilaki; Jane A Thanassi; Guangwei Yang; Andrea C Baines; Steven D Podos; Yongqing Huang; Mingjun Huang; Robert A Brodsky
Journal:  Haematologica       Date:  2016-11-03       Impact factor: 9.941

6.  Complement factor D haplodeficiency is associated with a reduced complement activation speed and diminished bacterial killing.

Authors:  Jeroen D Langereis; Renate G van der Molen; Corrie de Kat Angelino; Stefanie S Henriet; Marien I de Jonge; Irma Joosten; Annet Simons; Janneke Hm Schuurs-Hoeijmakers; Marcel van Deuren; Koen van Aerde; Michiel van der Flier
Journal:  Clin Transl Immunology       Date:  2021-04-03

7.  Plasma levels of complement proteins from the alternative pathway in patients with age-related macular degeneration are independent of Complement Factor H Tyr⁴⁰²His polymorphism.

Authors:  Aldacilene Souza Silva; Anderson Gustavo Teixeira; Lorena Bavia; Fabio Lin; Roberta Velletri; Rubens Belfort; Lourdes Isaac
Journal:  Mol Vis       Date:  2012-08-30       Impact factor: 2.367

Review 8.  Complement Factor D as a Strategic Target for Regulating the Alternative Complement Pathway.

Authors:  Jonathan Barratt; Ilene Weitz
Journal:  Front Immunol       Date:  2021-09-09       Impact factor: 7.561

  8 in total

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