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Literature DB >> 6539000

Dysfibrinogenemia (fibrinogen Dusard) associated with impaired fibrin-enhanced plasminogen activation.

H R Lijnen, J Soria, C Soria, D Collen, J P Caen.

Abstract

The fibrin-mediated enhancement of the activation of plasminogen by tissue-type plasminogen activator observed with normal fibrin, is strongly decreased with fibrin Dusard, although the binding of tissue-type plasminogen activator to this fibrin is normal. This impaired fibrin-mediated plasminogen activation is most likely related to the history of recurrent thrombosis and pulmonary embolism observed in this family.

Entities: Disease Gene

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Year: 1984 PMID： 6539000

Source DB: PubMed Journal: Thromb Haemost ISSN： 0340-6245 Impact factor: 5.249

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Cited

12 in total

1. NMR solution structure, stability, and interaction of the recombinant bovine fibrinogen alphaC-domain fragment.

Authors: Robert A Burton; Galina Tsurupa; Roy R Hantgan; Nico Tjandra; Leonid Medved
Journal: Biochemistry Date: 2007-06-23 Impact factor: 3.162

2. The relationship between the fibrinogen D domain self-association/cross-linking site (gammaXL) and the fibrinogen Dusart abnormality (Aalpha R554C-albumin): clues to thrombophilia in the "Dusart syndrome".

Authors: M W Mosesson; K R Siebenlist; J f Hainfeld; J S Wall; J Soria; C Soria; J P Caen
Journal: J Clin Invest Date: 1996-05-15 Impact factor: 14.808

3. Fibrinogen Dusart: electron microscopy of molecules, fibers and clots, and viscoelastic properties of clots.

Authors: J P Collet; J L Woodhead; J Soria; C Soria; M Mirshahi; J P Caen; J W Weisel
Journal: Biophys J Date: 1996-01 Impact factor: 4.033

Review 4. Fibrinogen, red blood cells, and factor XIII in venous thrombosis.

Authors: B L Walton; J R Byrnes; A S Wolberg
Journal: J Thromb Haemost Date: 2015-06 Impact factor: 5.824

5. Molecular basis for fibrinogen Dusart (A alpha 554 Arg-->Cys) and its association with abnormal fibrin polymerization and thrombophilia.

Authors: J Koopman; F Haverkate; J Grimbergen; S T Lord; M W Mosesson; J P DiOrio; K S Siebenlist; C Legrand; J Soria; C Soria
Journal: J Clin Invest Date: 1993-04 Impact factor: 14.808

Dysfibrinogenemia (fibrinogen Dusard) associated with impaired fibrin-enhanced plasminogen activation.

1. NMR solution structure, stability, and interaction of the recombinant bovine fibrinogen alphaC-domain fragment.

2. The relationship between the fibrinogen D domain self-association/cross-linking site (gammaXL) and the fibrinogen Dusart abnormality (Aalpha R554C-albumin): clues to thrombophilia in the "Dusart syndrome".

3. Fibrinogen Dusart: electron microscopy of molecules, fibers and clots, and viscoelastic properties of clots.

Review 4. Fibrinogen, red blood cells, and factor XIII in venous thrombosis.

5. Molecular basis for fibrinogen Dusart (A alpha 554 Arg-->Cys) and its association with abnormal fibrin polymerization and thrombophilia.

Review 6. Structure and function of human fibrinogen inferred from dysfibrinogens.

7. Congenital Afibrinogenemia presenting as antenatal intracranial bleed: a case report.

Review 8. Fibrinolysis and the control of blood coagulation.

Review 9. Clinical disorders of fibrinolysis: a critical review.

10. Hereditary thrombophilia.