Literature DB >> 6487548

Six cases of malignant atrophic papulosis (Degos' disease) occurring in one family.

L S Kisch, D P Bruynzeel.   

Abstract

A family is described in which a mother and five of her children were affected by malignant atrophic papulosis. This suggests that genetic factors might be involved in this condition.

Entities:  

Mesh:

Year:  1984        PMID: 6487548     DOI: 10.1111/j.1365-2133.1984.tb06611.x

Source DB:  PubMed          Journal:  Br J Dermatol        ISSN: 0007-0963            Impact factor:   9.302


  6 in total

1.  Diffuse atrophic papules and plaques, intermittent abdominal pain, paresthesias, and cardiac abnormalities in a 55-year-old woman.

Authors:  Brittany Oliver; Manfred Boehm; Douglas R Rosing; Lee S Shapiro; Daniel T Dempsey; Peter A Merkel; Chyi-Chia Richard Lee; Edward W Cowen
Journal:  J Am Acad Dermatol       Date:  2016-10-04       Impact factor: 11.527

2.  An atypical paediatric case of malignant atrophic papulosis (Köhlmeier-Degos disease).

Authors:  A Barabino; F Pesce; R Gatti; P Colotto; F Nobili; R Colacino; A Giampalmo
Journal:  Eur J Pediatr       Date:  1990-04       Impact factor: 3.183

3.  Renovascular hypertension in a child with Degos-Köhlmeier disease.

Authors:  F B Schade; L Monnens; J H Hendriks; G Rosenbusch
Journal:  Pediatr Radiol       Date:  1987

4.  Degos disease - malignant atrophic papulosis or cutaneointestinal lethal syndrome: rarity of the disease.

Authors:  Eduardo Pirolla; Felipe Fregni; Irene K Miura; Antonio Carlos Misiara; Fernando Almeida; Esdras Zanoni
Journal:  Clin Exp Gastroenterol       Date:  2015-04-16

5.  Clinical and laboratory prognosticators of atrophic papulosis (Degos disease): a systematic review.

Authors:  Justin D Lu; Muskaan Sachdeva; Orli M Silverberg; David Croitoru; Rebecca Levy; Lee Shapiro
Journal:  Orphanet J Rare Dis       Date:  2021-05-06       Impact factor: 4.123

Review 6.  Malignant atrophic papulosis (Köhlmeier-Degos disease) - a review.

Authors:  Athanasios Theodoridis; Evgenia Makrantonaki; Christos C Zouboulis
Journal:  Orphanet J Rare Dis       Date:  2013-01-14       Impact factor: 4.123

  6 in total

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