Literature DB >> 644530

Familial combined cellular and humoral immune defect with multisystem granulomata.

W H Perks, I S Petheram.   

Abstract

A brother and sister presented with recurrent respiratory infections. Investigations showed combined cellular and humoral immune defects and non-caseating granulomata in lungs, liver, lymph nodes, and skin. Despite antimycobacterial chemotherapy and corticosteroids in the brother and the additional treatment of human immunoglobulin injections in the sister both patients deteriorated with pulmonary and hepatic involvement.

Entities:  

Mesh：

Year:  1978        PMID： 644530      PMCID： PMC470855          DOI： 10.1136/thx.33.1.101

Source DB:  PubMed          Journal:  Thorax        ISSN： 0040-6376            Impact factor:   9.139


  16 in total

1.  PRIMARY "ACQUIRED" HYPOGAMMAGLOBULINEMIA; CLINICAL AND GENETIC ASPECTS OF NINE CASES.

Authors:  F A WOLLHEIM; S BELFRAGE; C COESTER; H LINDHOLM
Journal:  Acta Med Scand       Date:  1964-07

2.  Inherited "acquired" hypogammaglobulinaemia.

Authors:  F WOLLHEIM
Journal:  Lancet       Date:  1961-02-11       Impact factor: 79.321

3.  Syndrome of hypogammaglobulinemia, splenomegaly and hypersplenism.

Authors:  A S PRASAD; E REINER; C J WATSON
Journal:  Blood       Date:  1957-10       Impact factor: 22.113

4.  Agammaglobulinaemia.

Authors:  G H GRANT; W D WALLACE
Journal:  Lancet       Date:  1954-10-02       Impact factor: 79.321

5.  Elevation of serum angiotensin-converting enzyme in Gaucher's disease.

Authors:  J Lieberman; E Beutler
Journal:  N Engl J Med       Date:  1976-06-24       Impact factor: 91.245

6.  Agammaglobulinemia.

Authors:  A S PRASAD; D W KOZA
Journal:  Ann Intern Med       Date:  1954-09       Impact factor: 25.391

7.  Agammaglobulinemia.

Authors:  O C BRUTON
Journal:  Pediatrics       Date:  1952-06       Impact factor: 7.124

8.  Lymphocyte purine 5'-nucleotidase edficiency in primary hypogammaglobulinaemia.

Authors:  S M Johnson; M E North; G L Asherson; J Allsop; R W Watts; A D Webster
Journal:  Lancet       Date:  1977-01-22       Impact factor: 79.321

9.  Hereditary alterations in the immune response: coexistence of "agammaglobulinemia", acquired hypogammaglobulinemia and selective immunoglobulin deficiency in a sibship.

Authors:  R H Buckley; J B Sidbury
Journal:  Pediatr Res       Date:  1968-03       Impact factor: 3.756

10.  Familial hypogammaglobulinemia, splenomegaly and leukopenia. With a review of the etiological factors of the hypogammaglobulinemias.

Authors:  D S KUSHNER; A DUBIN; W P DONLON; D BRONSKY
Journal:  Am J Med       Date:  1960-07       Impact factor: 4.965
View more
  2 in total

1.  Acquired common variable hypogammaglobulinaemia and lymphoedema.

Authors:  S Lozewicz; G Morris; N Garbett; N Browse; B Slavin; P Cole
Journal:  Postgrad Med J       Date:  1988-01       Impact factor: 2.401

Review 2.  Development of granulomatous common variable immunodeficiency subsequent to infection with Toxoplasma gondii.

Authors:  S Mrusek; A Marx; J Kummerle-Deschner; N Tzaribachev; A Enders; U-N Riede; K Warnatz; G E Dannecker; S Ehl
Journal:  Clin Exp Immunol       Date:  2004-09       Impact factor: 4.330
  2 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.