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10 in total

1. Direct physical evidence for stabilization of branched-chain alpha-ketoacid dehydrogenase by thiamin pyrophosphate.

Authors: S C Heffelfinger; E T Sewell; L J Elsas; D J Danner
Journal: Am J Hum Genet Date: 1984-07 Impact factor: 11.025

2. Megavitamin therapy in inherited metabolic disorders.

Authors: S C Kalhan
Journal: Indian J Pediatr Date: 1981 Sep-Oct Impact factor: 1.967

3. Thiamin-responsive maple-syrup-urine disease: decreased affinity of the mutant branched-chain alpha-keto acid dehydrogenase for alpha-ketoisovalerate and thiamin pyrophosphate.

Authors: D T Chuang; L S Ku; R P Cox
Journal: Proc Natl Acad Sci U S A Date: 1982-05 Impact factor: 11.205

4. Decreased transport of ornithine across the inner mitochondrial membrane as a cause of hyperornithinaemia.

Authors: F A Hommes; C K Ho; R A Roesel; M E Coryell; B A Gordon
Journal: J Inherit Metab Dis Date: 1982 Impact factor: 4.982

5. Branched-chain ketoacid dehydrogenase activity and growth of normal and mutant human fibroblasts: the effect of branched-chain amino acid concentration in culture medium.

Authors: D J Danner; J H Priest
Journal: Biochem Genet Date: 1983-10 Impact factor: 1.890

6. Demonstration of a specific mitochondrial isovaleryl-CoA dehydrogenase deficiency in fibroblasts from patients with isovaleric acidemia.

Authors: W J Rhead; K Tanaka
Journal: Proc Natl Acad Sci U S A Date: 1980-01 Impact factor: 11.205

7. Absence of branched chain acyl-transferase as a cause of maple syrup urine disease.

Authors: D J Danner; N Armstrong; S C Heffelfinger; E T Sewell; J H Priest; L J Elsas
Journal: J Clin Invest Date: 1985-03 Impact factor: 14.808

Review 8. Thiamine-responsive inborn errors of metabolism.

Authors: M Duran; S K Wadman
Journal: J Inherit Metab Dis Date: 1985 Impact factor: 4.982

9. Identification of vitamin B1 metabolism as a tumor-specific radiosensitizing pathway using a high-throughput colony formation screen.

Authors: Gaganpreet S Tiwana; Remko Prevo; Francesca M Buffa; Sheng Yu; Daniel V Ebner; Alison Howarth; Lisa K Folkes; Balam Budwal; Kwun-Ye Chu; Lisa Durrant; Ruth J Muschel; W Gillies McKenna; Geoff S Higgins
Journal: Oncotarget Date: 2015-03-20

10. Linking vitamin B1 with cancer cell metabolism.

Authors: Jason A Zastre; Rebecca L Sweet; Bradley S Hanberry; Star Ye
Journal: Cancer Metab Date: 2013-07-24

10 in total