Literature DB >> 6288909

WDHA syndrome caused by VIP-producing ganglioneuroblastoma.

K Kudo, S Kitajima, H Munakata, S Yagihashi.   

Abstract

A 3 yr 11 mo-old girl showing classical symptoms of WDHA syndrome was transferred to our department of surgery. In preoperative examination, serum vasoactive intestinal peptide (VIP) was markedly elevated and pancreatic tumor was suspected. However, no tumor was found in the resected pancreas. Unfortunately, an unexpected adrenal tumor (ganglioneuroblastoma) was found in autopsy. The tumor was judged VIPO positive, immunohistochemically. This case was thought to be WDHA syndrome caused by VIPO-producing ganglioneuroblastoma (VIPoma).

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Year:  1982        PMID: 6288909     DOI: 10.1016/s0022-3468(82)80507-1

Source DB:  PubMed          Journal:  J Pediatr Surg        ISSN: 0022-3468            Impact factor:   2.545


  2 in total

1.  Adrenal ganglioneuroma-pheochromocytoma secreting vasoactive intestinal polypeptide.

Authors:  L N Contreras; D Budd; T S Yen; C Thomas; J B Tyrrell
Journal:  West J Med       Date:  1991-03

Review 2.  VIP secreting tumours in infancy. A review of radiological appearances.

Authors:  R P Davies; J P Slavotinek; S F Dorney
Journal:  Pediatr Radiol       Date:  1990
  2 in total

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