Unusual renal angiomyolipoma in tuberous sclerosis.

A patient with tuberous sclerosis and a normal intravenous urogram 5 years previously presented with a large and palpable upper pole renal mass. Since patients with tuberous sclerosis have small bilateral hamartomas, a Wilms' tumor was suspected. In retrospect, inhomogenous nephrograms should have alerted the radiologist to the multiplicity of other small lesions. Also, a partially lucent rim should have sustantiated that the lesion was not a Wilms' tumor.