Isolated right ventricular infarction with massive dilation: acquired Uhl's disease?

A patient had extensive isolated right ventricular infarction, which as the result of proximal occlusion of a small right coronary artery in a dominant left circumflex coronary arterial system, with minimal left-sided disease. A healed right ventricular infarction and Uhl's disease may have similar clinical and morphologic features. The sequence of events in our patient raises the question of whether coronary artery occlusion and myocardial infarction may be associated with a parchmentlike right ventricle. Damage to the right ventricular myocardium with subsequent superimposed chamber pressures and resulting dilation may lead to morphologic features similar to the parchment heart of Uhl's anomaly.