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20 in total

1. Liver transplantation for classical maple syrup urine disease: long-term follow-up in 37 patients and comparative United Network for Organ Sharing experience.

Authors: George V Mazariegos; D Holmes Morton; Rakesh Sindhi; Kyle Soltys; Navdeep Nayyar; Geoffrey Bond; Diana Shellmer; Benjamin Shneider; Jerry Vockley; Kevin A Strauss
Journal: J Pediatr Date: 2011-08-11 Impact factor: 4.406

2. Coadministration of branched-chain amino acids and lipopolysaccharide causes matrix metalloproteinase activation and blood-brain barrier breakdown.

Authors: Giselli Scaini; Meline O S Morais; Leticia S Galant; Francieli Vuolo; Dhébora M Dall'Igna; Matheus A B Pasquali; Vitor M Ramos; Daniel P Gelain; Jose Claudio F Moreira; Patrícia F Schuck; Gustavo C Ferreira; Francisco G Soriano; Felipe Dal-Pizzol; Emilio L Streck
Journal: Mol Neurobiol Date: 2014-01-05 Impact factor: 5.590

3. Abnormal amino acid metabolism and brain protein synthesis during neural development.

Authors: J V Hughes; T C Johnson
Journal: Neurochem Res Date: 1978-08 Impact factor: 3.996

4. Maple syrup urine disease (branched chain ketoaciduria).

Authors: P A Harper; P J Healy; J A Dennis
Journal: Am J Pathol Date: 1990-06 Impact factor: 4.307

5. Behavioral responses in rats submitted to chronic administration of branched-chain amino acids.

Authors: Giselli Scaini; Gabriela C Jeremias; Camila B Furlanetto; Diogo Dominguini; Clarissa M Comim; João Quevedo; Patrícia F Schuck; Gustavo C Ferreira; Emilio L Streck
Journal: JIMD Rep Date: 2013-11-09

Review 6. Interactions in the Metabolism of Glutamate and the Branched-Chain Amino Acids and Ketoacids in the CNS.

Authors: Marc Yudkoff
Journal: Neurochem Res Date: 2016-10-01 Impact factor: 3.996

7. Infantile spongy degeneration of the central nervous system associated with glycogen storage and markedly fatty liver.

Authors: Y Takei; G B Solitare
Journal: J Neurol Neurosurg Psychiatry Date: 1972-02 Impact factor: 10.154

8. Chemical changes in the spinal cord in Friedreich's ataxia and motor neurone disease.

Authors: N Robinson
Journal: J Neurol Neurosurg Psychiatry Date: 1968-08 Impact factor: 10.154

9. Inhibition by the branched-chain 2-oxo acids of the 2-oxoglutarate dehydrogenase complex in developing rat and human brain.

Authors: M S Patel
Journal: Biochem J Date: 1974-10 Impact factor: 3.857

10. Biochemical correlates of neuropsychiatric illness in maple syrup urine disease.

Authors: Emilie R Muelly; Gregory J Moore; Scott C Bunce; Julie Mack; Don C Bigler; D Holmes Morton; Kevin A Strauss
Journal: J Clin Invest Date: 2013-03-08 Impact factor: 14.808