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6 in total

1. Maple syrup urine disease: interrelations between branched-chain amino-, oxo- and hydroxyacids; implications for treatment; associations with CNS dysmyelination.

Authors: E Treacy; C L Clow; T R Reade; D Chitayat; O A Mamer; C R Scriver
Journal: J Inherit Metab Dis Date: 1992 Impact factor: 4.982

2. Branched chain amino acids induce apoptosis in neural cells without mitochondrial membrane depolarization or cytochrome c release: implications for neurological impairment associated with maple syrup urine disease.

Authors: P Jouvet; P Rustin; D L Taylor; J M Pocock; U Felderhoff-Mueser; N D Mazarakis; C Sarraf; U Joashi; M Kozma; K Greenwood; A D Edwards; H Mehmet
Journal: Mol Biol Cell Date: 2000-05 Impact factor: 4.138

Review 3. Inborn errors of metabolism: clues to understanding human behavioral disorders.

Authors: G S Omenn
Journal: Behav Genet Date: 1976-07 Impact factor: 2.805

4. Inhibition by the branched-chain 2-oxo acids of the 2-oxoglutarate dehydrogenase complex in developing rat and human brain.

Authors: M S Patel
Journal: Biochem J Date: 1974-10 Impact factor: 3.857

5. Maple syrup urine disease: branched-chain amino acid concentrations and metabolism in cultured human lymphoblasts.

Authors: S D Skaper; D P Molden; J E Seegmiller
Journal: Biochem Genet Date: 1976-08 Impact factor: 1.890

6. Differential effects of 2-oxo acids on pyruvate utilization and fatty acid synthesis in rat brain.

Authors: J B Clark; J M Land
Journal: Biochem J Date: 1974-04 Impact factor: 3.857

6 in total