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16 in total

1. Metabolic effects of propionate administration to normal and vitamin B12-deficient rats.

Authors: D L Williams; G H Spray; D H Williamson
Journal: Biochem J Date: 1971-01 Impact factor: 3.857

2. Methylmalonic acidemia controlled with oral administration of vitamin B12.

Authors: B A Gordon; R A Carson
Journal: Can Med Assoc J Date: 1976-08-07 Impact factor: 8.262

Review 3. [Methylmalonic aciduria. Classification, diagnosis and therapy (author's transl)].

Authors: D Leupold
Journal: Klin Wochenschr Date: 1977-01-15

4. The inhibition by methylmalonic acid of malate transport by the dicarboxylate carrier in rat liver mitochondria. A possible explantation for hypoglycemia in methylmalonic aciduria.

Authors: M L Halperin; C M Schiller; I B Fritz
Journal: J Clin Invest Date: 1971-11 Impact factor: 14.808

5. Metabolic effects of propionate in normal and vitamin B 12 -deficient rats.

Authors: D L Williams; G H Spray; R Hems; D H Williamson
Journal: Biochem J Date: 1971-09 Impact factor: 3.857

6. Deficiency of the iron-sulfur clusters of mitochondrial reduced nicotinamide-adenine dinucleotide-ubiquinone oxidoreductase (complex I) in an infant with congenital lactic acidosis.

Authors: R W Moreadith; M L Batshaw; T Ohnishi; D Kerr; B Knox; D Jackson; R Hruban; J Olson; B Reynafarje; A L Lehninger
Journal: J Clin Invest Date: 1984-09 Impact factor: 14.808

7. Mitochondrial dysfunction in mut methylmalonic acidemia.

Authors: Randy J Chandler; Patricia M Zerfas; Sara Shanske; Jennifer Sloan; Victoria Hoffmann; Salvatore DiMauro; Charles P Venditti
Journal: FASEB J Date: 2008-12-16 Impact factor: 5.191

Review 8. Methylmalonic and propionic acidemias: clinical management update.

Authors: Jamie L Fraser; Charles P Venditti
Journal: Curr Opin Pediatr Date: 2016-12 Impact factor: 2.856

Review 9. Methylmalonic acidemia: Current status and research priorities.

Authors: Xiaoyan Zhou; Yazhou Cui; Jinxiang Han
Journal: Intractable Rare Dis Res Date: 2018-05

10. Dietary therapy in two patients with vitamin B12-unresponsive methylmalonic acidemia.

Authors: T Satoh; K Narisawa; Y Igarashi; T Saitoh; K Hayasaka; Y Ichinohazama; H Onodera; K Tada; K Oohara
Journal: Eur J Pediatr Date: 1981-02 Impact factor: 3.183