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23 in total

1. Biosynthesis and maturation of peroxisomal beta-oxidation enzymes in fibroblasts in relation to the Zellweger syndrome and infantile Refsum disease.

Authors: A W Schram; A Strijland; T Hashimoto; R J Wanders; R B Schutgens; H van den Bosch; J M Tager
Journal: Proc Natl Acad Sci U S A Date: 1986-08 Impact factor: 11.205

2. Deficient oxidation of trihydroxycoprostanic acid in liver homogenates from patients with peroxisomal diseases.

Authors: M Casteels; C W Van Roermund; L Schepers; L Govaert; H J Eyssen; G P Mannaerts; R J Wanders
Journal: J Inherit Metab Dis Date: 1989 Impact factor: 4.982

3. Infantile Refsum's disease: biochemical findings suggesting multiple peroxisomal dysfunction.

Authors: B T Poll-The; J M Saudubray; H Ogier; R B Schutgens; R J Wanders; G Schrakamp; H van den Bosch; J M Trijbels; A Poulos; H W Moser
Journal: J Inherit Metab Dis Date: 1986 Impact factor: 4.982

Review 4. Peroxisomal disorders: a newly recognised group of genetic diseases.

Authors: R B Schutgens; H S Heymans; R J Wanders; H van den Bosch; J M Tager
Journal: Eur J Pediatr Date: 1986-02 Impact factor: 3.183

5. An inborn error of bile acid synthesis (3beta-hydroxy-delta5-C27-steroid dehydrogenase deficiency) presenting as malabsorption leading to rickets.

Authors: A K Akobeng; P T Clayton; V Miller; M Super; A G Thomas
Journal: Arch Dis Child Date: 1999-05 Impact factor: 3.791

10. Sulphated bile acids in duodenal juice of healthy infants and children compared with sulphated bile acids in paediatric patients with various gastroenterological diseases.

Authors: K H Niessen; M Teufel; G Brügmann
Journal: Gut Date: 1984-01 Impact factor: 23.059

Trihydroxycoprostanic acid in the duodenal fluid of two children with intrahepatic bile duct anomalies.

1. Biosynthesis and maturation of peroxisomal beta-oxidation enzymes in fibroblasts in relation to the Zellweger syndrome and infantile Refsum disease.

2. Deficient oxidation of trihydroxycoprostanic acid in liver homogenates from patients with peroxisomal diseases.

3. Infantile Refsum's disease: biochemical findings suggesting multiple peroxisomal dysfunction.

Review 4. Peroxisomal disorders: a newly recognised group of genetic diseases.

5. An inborn error of bile acid synthesis (3beta-hydroxy-delta5-C27-steroid dehydrogenase deficiency) presenting as malabsorption leading to rickets.

6. Paucity of interlobular bile ducts: getting to know it better.

7. Defective peroxisomal cleavage of the C27-steroid side chain in the cerebro-hepato-renal syndrome of Zellweger.

8. Postnatal physiologic hypercholemia in both premature and full-term infants.

9. Taurocholate pool size and distribution in the fetal rat.

10. Sulphated bile acids in duodenal juice of healthy infants and children compared with sulphated bile acids in paediatric patients with various gastroenterological diseases.