Literature DB >> 5059566

Galactose utilization in galactosemia.

J C Petricciani, M K Binder, C R Merril, M R Geier.   

Abstract

Cultures of human galactosemic fibroblasts without detectable transferase activity were able to convert [1-(14)C]galactose to (14)CO(2) to the same extent as normal cells, but did so at a significantly slower rate. The utilization of galactose in both normal and galactosemic cells was strongly inhibited by glucose at physiologic concentrations.

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Year:  1972        PMID： 5059566     DOI： 10.1126/science.175.4028.1368

Source DB:  PubMed          Journal:  Science        ISSN： 0036-8075            Impact factor:   47.728


  4 in total

1.  Oxidation of galactose by galactose-1-phosphate uridyltransferase-deficient lymphoblasts.

Authors:  C Yager; J Gibson; B States; L J Elsas; S Segal
Journal:  J Inherit Metab Dis       Date:  2001-08       Impact factor: 4.982

2.  CO2 production from galactose in galactose-1-phosphate uridyl transferase-deficient Escherichia coli.

Authors:  R J LaPolla; M R Geier; T B Friedman; C R Merril
Journal:  J Bacteriol       Date:  1975-10       Impact factor: 3.490

3.  Clinical and biochemical evidence of skeletal muscle involvement in galactose-1-phosphate uridyl transferase deficiency.

Authors:  N Bresolin; G P Comi; F Fortunato; G Meola; A Gallanti; A Tajana; M Velicogna; E F Gonano; P Ninfali; S Pifferi
Journal:  J Neurol       Date:  1993-05       Impact factor: 4.849

4.  Galactose metabolism in transferase-deficient galactosaemic and normal long-term lymphoid cell lines.

Authors:  N G Beratis; L Wilbur
Journal:  J Inherit Metab Dis       Date:  1987       Impact factor: 4.982
  4 in total

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