Literature DB >> 5049818

Progressive familial cholestatic cirrhosis and bile acid metabolism.

C N Williams, R Kaye, L Baker, R Hurwitz, J R Senior.   

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Year:  1972        PMID: 5049818     DOI: 10.1016/s0022-3476(72)80175-6

Source DB:  PubMed          Journal:  J Pediatr        ISSN: 0022-3476            Impact factor:   4.406


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  13 in total

1.  Partial internal biliary diversion for patients with progressive familial intrahepatic cholestasis type 1.

Authors:  Kyoko Mochizuki; Masayuki Obatake; Mitsuhisa Takatsuki; Akiko Nakatomi; Tomayoshi Hayashi; Sadayuki Okudaira; Susumu Eguchi
Journal:  Pediatr Surg Int       Date:  2012-01       Impact factor: 1.827

2.  Progressive intrahepatic cholestasis (Byler's disease): case report.

Authors:  R De Vos; C de Wolf-Peeters; V Desmet; E Eggermont; K Van Acker
Journal:  Gut       Date:  1975-12       Impact factor: 23.059

3.  Localization of a recessive gene for North American Indian childhood cirrhosis to chromosome region 16q22-and identification of a shared haplotype.

Authors:  C Bétard; A Rasquin-Weber; C Brewer; E Drouin; S Clark; A Verner; C Darmond-Zwaig; J Fortin; J Mercier; P Chagnon; T M Fujiwara; K Morgan; A Richter; T J Hudson; G A Mitchell
Journal:  Am J Hum Genet       Date:  2000-05-11       Impact factor: 11.025

4.  Severe familial intrahepatic cholestasis.

Authors:  M Odiévre; M Gautier; M Hadchouel; D Alagille
Journal:  Arch Dis Child       Date:  1973-10       Impact factor: 3.791

5.  Pediatric gastroenterology 1/1/69-12/31/75: a review. Part II. The liver and biliary tract.

Authors:  A Finley; M Andorsky; M Davidson
Journal:  Am J Dig Dis       Date:  1977-02

6.  Fatal familial cholestatic syndrome in Greenland Eskimo children. A histomorphological analysis of 16 cases.

Authors:  K Ornvold; I M Nielsen; H Poulsen
Journal:  Virchows Arch A Pathol Anat Histopathol       Date:  1989

7.  Investigation of serum bile acids; seven patients with Alagille syndrome.

Authors:  K Obinata; N Nakatsu; T Watanabe; S Niijima; O Arisaka; H Sasaki; H Nittono; K Yabuta; T Miyano
Journal:  Eur J Pediatr       Date:  1985-09       Impact factor: 3.183

8.  Altered bile acid metabolism in primary biliary cirrhosis.

Authors:  R Raedsch; B H Lauterburg; A F Hofmann
Journal:  Dig Dis Sci       Date:  1981-05       Impact factor: 3.199

9.  Orthotopic liver transplantation in children: two-year experience with 47 patients.

Authors:  J C Gartner; B J Zitelli; J J Malatack; B W Shaw; S Iwatsuki; T E Starzl
Journal:  Pediatrics       Date:  1984-07       Impact factor: 7.124

10.  Pathology of chronic vitamin E deficiency in fatal familial intrahepatic cholestasis (Byler disease).

Authors:  K Saito; S Matsumoto; T Yokoyama; M Okaniwa; S Kamoshita
Journal:  Virchows Arch A Pathol Anat Histol       Date:  1982-08
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