Literature DB >> 5016650

Isolation and identification of methylcitrate, a major metabolic product of propionate in patients with propionic acidemia.

T Ando, K Rasmussen, J M Wright, W L Nyhan.   

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Year:  1972        PMID： 5016650

Source DB:  PubMed          Journal:  J Biol Chem        ISSN： 0021-9258            Impact factor:   5.157


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  28 in total

1.  Integrated Omic Analysis of a Guinea Pig Model of Heart Failure and Sudden Cardiac Death.

Authors:  D Brian Foster; Ting Liu; Kai Kammers; Robert O'Meally; Ni Yang; Kyriakos N Papanicolaou; C Conover Talbot; Robert N Cole; Brian O'Rourke
Journal:  J Proteome Res       Date:  2016-08-03       Impact factor: 4.466

2.  Inter-relations between 3-hydroxypropionate and propionate metabolism in rat liver: relevance to disorders of propionyl-CoA metabolism.

Authors:  Kirkland A Wilson; Yong Han; Miaoqi Zhang; Jeremy P Hess; Kimberly A Chapman; Gary W Cline; Gregory P Tochtrop; Henri Brunengraber; Guo-Fang Zhang
Journal:  Am J Physiol Endocrinol Metab       Date:  2017-06-20       Impact factor: 4.310

3.  Mild form of methylmalonic aciduria misdiagnosed as propionic acidaemia during a ketotic crisis.

Authors:  I T de Almeida; M Duran; M F Silva; R Portela; A Cabral; T Tasso; F Eusébio; C Silveira
Journal:  J Inherit Metab Dis       Date:  1991       Impact factor: 4.982

Review 4.  Enzyme complexity in intermediary metabolism.

Authors:  Emile Van Schaftingen; Maria Veiga-da-Cunha; Carole L Linster
Journal:  J Inherit Metab Dis       Date:  2015-02-21       Impact factor: 4.982

5.  3-hydroxypropionate: significance of -oxidation of propionate in patients with propionic acidemia and methylmalonic acidemia.

Authors:  T Ando; K Rasmussen; W L Nyhan; D Hull
Journal:  Proc Natl Acad Sci U S A       Date:  1972-10       Impact factor: 11.205

6.  Identification of the stereoisomeric configurations of methylcitric acid produced by si-citrate synthase and methylcitrate synthase using capillary gas chromatography-mass spectrometry.

Authors:  J P van Rooyen; L J Mienie; E Erasmus; W J De Wet; D Ketting; M Duran; S K Wadman
Journal:  J Inherit Metab Dis       Date:  1994       Impact factor: 4.982

7.  Enamel defects and salivary methylmalonate in methylmalonic acidemia.

Authors:  C W Bassim; J T Wright; J P Guadagnini; R Muralidharan; J Sloan; D L Domingo; C P Venditti; T C Hart
Journal:  Oral Dis       Date:  2009-01-09       Impact factor: 3.511

8.  Hudson memorial lecture. Neonatal management of organic acidurias. Clinical update.

Authors:  J M Saudubray; H Ogier; C Charpentier; E Depondt; F X Coudé; A Munnich; G Mitchell; F Rey; J Rey; J Frézal
Journal:  J Inherit Metab Dis       Date:  1984       Impact factor: 4.982

9.  Stimulation of ketogenesis by propionate in isolated rat hepatocytes: an explanation for ketosis associated with propionic acidaemia and methylmalonic acidaemia?

Authors:  P Rosario; J M Medina
Journal:  J Inherit Metab Dis       Date:  1982       Impact factor: 4.982

10.  Long-term rescue of a lethal murine model of methylmalonic acidemia using adeno-associated viral gene therapy.

Authors:  Randy J Chandler; Charles P Venditti
Journal:  Mol Ther       Date:  2009-10-27       Impact factor: 11.454
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