Literature DB >> 4975021

Gangliosidoses.

L Svennerholm.   

Abstract

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Year:  1969        PMID: 4975021      PMCID: PMC1187526          DOI: 10.1042/bj1110006p

Source DB:  PubMed          Journal:  Biochem J        ISSN: 0264-6021            Impact factor:   3.857


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  6 in total

1.  THE FEEDBACK CONTROL OF SUGAR NUCLEOTIDE BIOSYNTHESIS IN LIVER.

Authors:  S KORNFELD; R KORNFELD; E F NEUFELD; P J O'BRIEN
Journal:  Proc Natl Acad Sci U S A       Date:  1964-08       Impact factor: 11.205

2.  METABOLISM OF GLUCOCEREBROSIDES. II. EVIDENCE OF AN ENZYMATIC DEFICIENCY IN GAUCHER'S DISEASE.

Authors:  R O BRADY; J N KANFER; D SHAPIRO
Journal:  Biochem Biophys Res Commun       Date:  1965-01-18       Impact factor: 3.575

3.  STRUCTURE COMPARISON OF THE MAJOR MONOSIALOGANGLIOSIDES FROM BRAINS OF NORMAL HUMAN, GARGOYLISM, AND LATE INFANTILE SYSTEMIC LIPIDOSIS. I.

Authors:  R LEDEEN; K SALSMAN; J GONATAS; A TAGHAVY
Journal:  J Neuropathol Exp Neurol       Date:  1965-04       Impact factor: 3.685

4.  [A disorder of ganglioside metabolism with storage of ceramide lactoside, monosialo ceramide lactoside and Tay-Sachs ganglioside in the brain].

Authors:  H Pilz; K Sandhoff; H Jatzkewitz
Journal:  J Neurochem       Date:  1966-12       Impact factor: 5.372

5.  Enzymatic hydrolysis of sphingolipids. VII. Hydrolysis of gangliosides by a neuraminidase from calf brain.

Authors:  Z Leibovitz; S Gatt
Journal:  Biochim Biophys Acta       Date:  1968-01-10

6.  Generalized gangliosidosis: beta-galactosidase deficiency.

Authors:  S Okada; J S O'Brien
Journal:  Science       Date:  1968-05-31       Impact factor: 47.728

  6 in total
  1 in total

1.  [Infantile amaurotic idiocy and related forms as ganglioside storage diseases].

Authors:  K Sandhoff; H Jatzkewitz; G Peters
Journal:  Naturwissenschaften       Date:  1969-07
  1 in total

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