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13 in total

1. The requirements of the brain for some amino acids.

Authors: G Baños; P M Daniel; S R Moorhouse; O E Pratt
Journal: J Physiol Date: 1975-04 Impact factor: 5.182

2. Neonatal hyperammonaemia with complete absence of liver carbamyl phosphate synthetase activity.

Authors: S Mantagos; S Tsagaraki; E A Burgess; V Oberholzer; T Palmer; J Sacks; S Baibas; T Valaes
Journal: Arch Dis Child Date: 1978-03 Impact factor: 3.791

3. Hyperammonemia through deficiency of ornithine carbamyl transferase.

Authors: J P Farriaux; J L Dhondt; L Cathelineau; J Ratel; G Fontaine
Journal: Z Kinderheilkd Date: 1974

4. Hyperammonaemia in 20 families. Biochemical and genetical survey, including investigations in 3 new families.

Authors: T Palmer; V G Oberholzer; E A Burgess; L J Butler; B Levin
Journal: Arch Dis Child Date: 1974-06 Impact factor: 3.791

5. Variants of citrullinaemia.

Authors: H Wick; C Bachmann; R Baumgartner; T Brechbühler; J P Colombo; U Wiesmann; M J Mihatsch; H Ohnacker
Journal: Arch Dis Child Date: 1973-08 Impact factor: 3.791

6. Enzyme inhibition as a possible cause of secondary increases in metabolite levels in patients with inborn errors of metabolism.

Authors: T Palmer; M Ameen
Journal: J Inherit Metab Dis Date: 1980 Impact factor: 4.982

Hereditary metabolic disorders of the urea cycle.

1. The requirements of the brain for some amino acids.

2. Neonatal hyperammonaemia with complete absence of liver carbamyl phosphate synthetase activity.

3. Hyperammonemia through deficiency of ornithine carbamyl transferase.

4. Hyperammonaemia in 20 families. Biochemical and genetical survey, including investigations in 3 new families.

5. Variants of citrullinaemia.

6. Enzyme inhibition as a possible cause of secondary increases in metabolite levels in patients with inborn errors of metabolism.

7. Plasma ammonia levels in newborn infants admitted to an intensive care baby unit.

8. Synthesis of urea after stimulation with amino acids: relation to liver function.

9. Citrulline synthesis in rat tissues and liver content of carbamoyl phosphate and ornithine.

10. Acute neonatal and benign citrullinaemia in one sibship.