Literature DB >> 4860468

A cerebroside sulphotransferase deficiency in a human disorder of myelin.

B K Bachhawat, J Austin, D Armstrong.   

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Year:  1967        PMID: 4860468      PMCID: PMC1270641          DOI: 10.1042/bj1040015c

Source DB:  PubMed          Journal:  Biochem J        ISSN: 0264-6021            Impact factor:   3.857


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  7 in total

1.  A CONTROLLED STUDY OF ENZYMIC ACTIVITIES IN THREE HUMAN DISORDERS OF GLYCOLIPID METABOLISM.

Authors:  J H AUSTIN; A S BALASUBRAMANIAN; T N PATTABIRAMAN; S SARASWATHI; D K BASU; B K BACHHAWAT
Journal:  J Neurochem       Date:  1963-12       Impact factor: 5.372

2.  STUDIES IN GLOBOID (KRABBE) LEUKODYSTROPHY. II. CONTROLLED THIN-LAYER CHROMATOGRAPHIC STUDIES OF GLOBOID BODY FRACTIONS IN SEVEN PATIENTS.

Authors:  J H AUSTIN
Journal:  J Neurochem       Date:  1963-12       Impact factor: 5.372

3.  ENZYMIC TRANSFER OF SULPHATE FROM 3'-PHOSPHOADENOSINE 5'-PHOSPHOSULPHATE TO MUCOPOLYSACCHARIDES IN RAT BRAIN.

Authors:  A S BALASUBRAMANIAN; B K BACHHAWAT
Journal:  J Neurochem       Date:  1964-12       Impact factor: 5.372

4.  Formation of cerebroside sulphate from 3'-phosphoadenosine 5'-phosphosulphate in sheep brain.

Authors:  A S Balasubramanian; B K Bachhawat
Journal:  Biochim Biophys Acta       Date:  1965-07-07

5.  Metachromatic form of diffuse cerebral sclerosis. V. The nature and significance of low sulfatase activity: a controlled study of brain, liver and kidney in four patients with metachromatic leukodystrophy (MLD).

Authors:  J Austin; D Armstrong; L Shearer
Journal:  Arch Neurol       Date:  1965-12

Review 6.  STUDIES IN GLOBOID (KRABBE) LEUKODYSTROPHY. I. THE SIGNIFICANCE OF LIPID ABNORMALITIES IN WHITE MATTER IN 8 GLOBOID AND 13 CONTROL PATIENTS.

Authors:  J AUSTIN
Journal:  Arch Neurol       Date:  1963-09

7.  Studies on enzymic synthesis of cerebroside sulphate from 3'-phosphoadenosine-5'-phosphosulphate.

Authors:  A S Balasubramanian; B K Bachhawat
Journal:  Indian J Biochem       Date:  1965-12
  7 in total
  1 in total

1.  Leucodystrophy in mink.

Authors:  H A Andersen; B Palludan
Journal:  Acta Neuropathol       Date:  1968-11-01       Impact factor: 17.088

  1 in total

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