Literature DB >> 4690914

Electrophoretic study of hexosaminidases. Hexosaminidase C.

L Poenaru, J C Dreyfus.   

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Year:  1973        PMID: 4690914     DOI: 10.1016/0009-8981(73)90486-5

Source DB:  PubMed          Journal:  Clin Chim Acta        ISSN: 0009-8981            Impact factor:   3.786


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  18 in total

Review 1.  Biochemistry and genetics of gangliosidoses.

Authors:  K Sandhoff; H Christomanou
Journal:  Hum Genet       Date:  1979       Impact factor: 4.132

2.  Biochemical characterization of beta-hexosaminidase in different biological specimens from eleven patients with GM2-gangliosidosis B1 variant.

Authors:  M G Ribeiro; R A Pinto; M R Dos Santos; M Maia; M C Sá Miranda
Journal:  J Inherit Metab Dis       Date:  1991       Impact factor: 4.982

3.  Characterization of Hex S, the major residual beta hexosaminidase activity in type O Gm2 gangliosidosis (Sandhoff-Jatzkewitz disease).

Authors:  J U Ikonne; M C Rattazzi; R J Desnick
Journal:  Am J Hum Genet       Date:  1975-09       Impact factor: 11.025

Review 4.  Glycosphingolipid hydrolases: properties and molecular genetics.

Authors:  M Wan Ho; A G Norden; J A Alhadeff; J S O'Brien
Journal:  Mol Cell Biochem       Date:  1977-10-07       Impact factor: 3.396

5.  Characterization of a variant of beta-hexosaminidase: "hexosaminidase Paris".

Authors:  J C Dreyfus; L Poenaru; M Vibert; N Ravise; J Boue
Journal:  Am J Hum Genet       Date:  1977-05       Impact factor: 11.025

6.  Purification of normal human urinary N-acetyl-beta-hexosaminidase A by affinity chromatography.

Authors:  D K Banerjee; D Basu
Journal:  Biochem J       Date:  1975-01       Impact factor: 3.857

7.  Studies on human N-acetyl-Beta-d-hexosaminidase C separated from neonatal brain.

Authors:  G T Besley; D M Broadhead
Journal:  Biochem J       Date:  1976-04-01       Impact factor: 3.857

8.  Separation of three isoenzymes of N-acetyl-beta-D-hexosaminidase from human tissues by cellulose acetate membrane electrophoresis.

Authors:  A Westwood; D N Raine
Journal:  J Clin Pathol       Date:  1974-11       Impact factor: 3.411

9.  Characterization of a new model of GM2-gangliosidosis (Sandhoff's disease) in Korat cats.

Authors:  E A Neuwelt; W G Johnson; N K Blank; M A Pagel; C Maslen-McClure; M J McClure; P M Wu
Journal:  J Clin Invest       Date:  1985-08       Impact factor: 14.808

10.  Hexosaminidase isozyme in type O Gm2 gangliosidosis (Sandhoff-Jatzkewitz disease).

Authors:  E Beutler; W Kuhl; D Comings
Journal:  Am J Hum Genet       Date:  1975-09       Impact factor: 11.025

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