Literature DB >> 4593851

Spongy degeneration of the central nervous system (van Bogaert and Bertrand type; Canavan's disease). A review.

M Adachi, L Schneck, J Cara, B W Volk.   

Abstract

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Year:  1973        PMID： 4593851     DOI： 10.1016/s0046-8177(73)80098-x

Source DB:  PubMed          Journal:  Hum Pathol        ISSN： 0046-8177            Impact factor:   3.466


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  39 in total

1.  Organized inclusions in astrocytic and amorphous inclusions in neuronal mitochondria of human frontal brain tissue.

Authors:  H Herrlinger; A P Anzil; K Blinzinger
Journal:  Cell Tissue Res       Date:  1975       Impact factor: 5.249

2.  Experimental spongy degeneration in calves.

Authors:  D Y Cho; H W Leipold
Journal:  Acta Neuropathol       Date:  1977-08-16       Impact factor: 17.088

3.  Redirecting N-acetylaspartate metabolism in the central nervous system normalizes myelination and rescues Canavan disease.

Authors:  Dominic J Gessler; Danning Li; Hongxia Xu; Qin Su; Julio Sanmiguel; Serafettin Tuncer; Constance Moore; Jean King; Reuben Matalon; Guangping Gao
Journal:  JCI Insight       Date:  2017-02-09

Review 4.  N-Acetylaspartate in the CNS: from neurodiagnostics to neurobiology.

Authors:  John R Moffett; Brian Ross; Peethambaran Arun; Chikkathur N Madhavarao; Aryan M A Namboodiri
Journal:  Prog Neurobiol       Date:  2007-01-05       Impact factor: 11.685

5.  Pathophysiology and Treatment of Canavan Disease.

Authors:  David Pleasure; Fuzheng Guo; Olga Chechneva; Peter Bannerman; Jennifer McDonough; Travis Burns; Yan Wang; Vanessa Hull
Journal:  Neurochem Res       Date:  2018-12-08       Impact factor: 3.996

6.  Spongy degeneration in the central nervous system of domestic animals. Part I: Morphology.

Authors:  P T Hooper
Journal:  Acta Neuropathol       Date:  1975       Impact factor: 17.088

7.  Long-term follow-up after gene therapy for canavan disease.

Authors:  Paola Leone; David Shera; Scott W J McPhee; Jeremy S Francis; Edwin H Kolodny; Larissa T Bilaniuk; Dah-Jyuu Wang; Mitra Assadi; Olga Goldfarb; H Warren Goldman; Andrew Freese; Deborah Young; Matthew J During; R Jude Samulski; Christopher G Janson
Journal:  Sci Transl Med       Date:  2012-12-19       Impact factor: 17.956

8.  Ultrastructural findings in maple syrup urine disease in Poll Hereford calves.

Authors:  P A Harper; P J Healy; J A Dennis
Journal:  Acta Neuropathol       Date:  1986       Impact factor: 17.088

9.  Nur7 is a nonsense mutation in the mouse aspartoacylase gene that causes spongy degeneration of the CNS.

Authors:  Maria Traka; Robert L Wollmann; Sonia R Cerda; Jason Dugas; Ben A Barres; Brian Popko
Journal:  J Neurosci       Date:  2008-11-05       Impact factor: 6.167

Review 10.  Gene Therapy for the Treatment of Neurological Disorders: Metabolic Disorders.

Authors:  Dominic J Gessler; Guangping Gao
Journal:  Methods Mol Biol       Date:  2016
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