Literature DB >> 4554588

Subacute spongiform encephalopathy and its relation to Jakob-Creutzfeldt disease: report on six cases.

Y Goldhammer, J J Bubis, I Sarova-Pinhas, J Braham.   

Abstract

An account is given of six cases of Jakob-Creutzfeldt disease confirmed at necropsy. The rapid fatal outcome within three months was typical of the variety designated subacute spongiform encephalopathy (Nevin-Jones). The characteristic EEG changes were found to be of great value in making an early diagnosis and, together with akinetic mutism and myoclonus, constituted an easily recognizable picture. Treatment with idoxyuridine was ineffective in one case in which electronmicroscopy of brain biopsy material supported the diagnosis.

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Year:  1972        PMID： 4554588      PMCID： PMC493954          DOI： 10.1136/jnnp.35.1.1

Source DB:  PubMed          Journal:  J Neurol Neurosurg Psychiatry        ISSN： 0022-3050            Impact factor:   10.154


  27 in total

1.  CREUTZFELDT-JAKOB'S DISEASE. CLINICOPATHOLOGIC REPORT OF 15 CASES AND REVIEW OF THE LITERATURE (WITH SPECIAL REFERENCE TO A RELATED DISORDER DESIGNATED AS SUBACUTE SPONGIFORM ENCEPHALOPATHY).

Authors:  H SIEDLER; N MALAMUD
Journal:  J Neuropathol Exp Neurol       Date:  1963-07       Impact factor: 3.685

2.  Rapidly progressive cerebral degeneration (subacute vascular encephalopathy) with mental disorder, focal disturbances, and myoclonic epilepsy.

Authors:  D P JONES; S NEVIN
Journal:  J Neurol Neurosurg Psychiatry       Date:  1954-05       Impact factor: 10.154

3.  Creutzfeldt-Jakob disease. The neuropathology of a transmission experiment.

Authors:  E Beck; P M Daniel; W B Matthews; D L Stevens; M P Alpers; D M Asher; D C Gajdusek; C J Gibbs
Journal:  Brain       Date:  1969       Impact factor: 13.501

4.  Creutzfeldt-Jakob disease (spongiform encephalopathy): transmission to the chimpanzee.

Authors:  C J Gibbs; D C Gajdusek; D M Asher; M P Alpers; E Beck; P M Daniel; W B Matthews
Journal:  Science       Date:  1968-07-26       Impact factor: 47.728

5.  Experimental transmission of a Kuru-like syndrome to chimpanzees.

Authors:  D C Gajdusek; C J Gibbs; M Alpers
Journal:  Nature       Date:  1966-02-19       Impact factor: 49.962

6.  [Symposium on presenile spongy encephalopathies. Synthesis of histopathologic contributions].

Authors:  H Jacob; L Van Bogaert
Journal:  Acta Neuropathol       Date:  1967       Impact factor: 17.088

7.  Some electron microscopical observations on status spongiosus.

Authors:  M Kidd
Journal:  Acta Neuropathol       Date:  1967       Impact factor: 17.088

8.  [Spongy encephalopathy of presenility and Creutzfeldt-Jakob syndrome].

Authors:  S Brion
Journal:  Acta Neuropathol       Date:  1967       Impact factor: 17.088

9.  [On a peculiar form of Creutzfeldt-Jakob disease, with anatomo-clinical dissociation].

Authors:  H Terzian; N Rizzuto; L Patarnello; J J Martin
Journal:  Acta Neuropathol       Date:  1967       Impact factor: 17.088

10.  Infection as the etiology of spongiform encephalopathy (Creutzfeldt-Jakob disease).

Authors:  C J Gibbs; D C Gajdusek
Journal:  Science       Date:  1969-09-05       Impact factor: 47.728
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  8 in total

Review 1.  Creutzfeldt-Jakob disease among Libyan Jews.

Authors:  A D Korczyn
Journal:  Eur J Epidemiol       Date:  1991-09       Impact factor: 8.082

2.  [The clinical syndrome of presenile idiopathic encephalopathy ("Jakob-Creutzfeldt-syndrome") or spongiform encephalopathy (author's transl)].

Authors:  R Meyendorf; C Förster
Journal:  Arch Psychiatr Nervenkr (1970)       Date:  1973-11-27

3.  Subacute spongiform encephalopathy. Electron microscopic studies.

Authors:  J J Bubis; Y Goldhammer; J Braham
Journal:  J Neurol Neurosurg Psychiatry       Date:  1972-12       Impact factor: 10.154

4.  The ataxic (cerebellar) form of Creutzfeldt-Jakob disease.

Authors:  K Jellinger; W D Heiss; E Deisenhammer
Journal:  J Neurol       Date:  1974       Impact factor: 4.849

5.  Clinical heterogeneity and unusual presentations of Creutzfeldt-Jakob disease in Jewish patients with the PRNP codon 200 mutation.

Authors:  J Chapman; P Brown; L G Goldfarb; A Arlazoroff; D C Gajdusek; A D Korczyn
Journal:  J Neurol Neurosurg Psychiatry       Date:  1993-10       Impact factor: 10.154

6.  Electroencephalographic and clinicopathological studies on Creutzfeldt-Jakob syndrome.

Authors:  K Goto; H Umezaki; M Suetsugu
Journal:  J Neurol Neurosurg Psychiatry       Date:  1976-10       Impact factor: 10.154

7.  Jakob-Creutzfeldt disease. Modification of clinical and electroencephalographic activity with methylphenidate and diazepam.

Authors:  F Elliott; C Gardner-Thorpe; D D Barwick; J B Foster
Journal:  J Neurol Neurosurg Psychiatry       Date:  1974-08       Impact factor: 10.154

Review 8.  Prions and related neurological diseases.

Authors:  M Pocchiari
Journal:  Mol Aspects Med       Date:  1994
  8 in total

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