Literature DB >> 4336232

Ketosis in hepatic glycogenosis.

J Fernandes, N A Pikaar.   

Abstract

Entities:  

Mesh：

Substances：

Year:  1972        PMID： 4336232      PMCID： PMC1647981          DOI： 10.1136/adc.47.251.41

Source DB:  PubMed          Journal:  Arch Dis Child        ISSN： 0003-9888            Impact factor:   3.791


× No keyword cloud information.
  18 in total

1.  AMYLO-1,6-GLUCOSIDASE ACTIVITY IN NORMAL LEUCOCYTES AND IN LEUCOCYTES OF PATIENTS WITH GLYCOGEN-STORAGE DISEASE.

Authors:  F HUIJING
Journal:  Clin Chim Acta       Date:  1964-03       Impact factor: 3.786

2.  STUDIES ON THE UTILIZATION OF HEXOSES IN LIVER GLYCOGEN DISEASE.

Authors:  J FERNANDES; J H VAN DE KAMER
Journal:  Pediatrics       Date:  1965-03       Impact factor: 7.124

3.  The glycogenoses. Further observations on glycogen in erythrocytes of patients with glycogenosis.

Authors:  J B SIDBURY; R GITZELMANN; J FISHER
Journal:  Helv Paediatr Acta       Date:  1961-12

4.  STUDIES OF GLYCOGEN METABOLISM IN LIVER GLYCOGEN DISEASE (VON GIERKE'S DISEASE): SIX CASES WITH SIMILAR METABOLIC ABNORMALITIES AND RESPONSES TO GLUCAGON.

Authors:  J E Sokal; C U Lowe; E J Sarcione; L L Mosovich; B H Doray
Journal:  J Clin Invest       Date:  1961-02       Impact factor: 14.808

5.  Studies in liver glycogen disease. Effects of glucagon and other agents on metabolic pattern and clinical status.

Authors:  C U LOWE; J E SOKAL; L L MOSOVICH; E J SARCIONE; B H DORAY
Journal:  Am J Med       Date:  1962-07       Impact factor: 4.965

6.  Splanchnic metabolism in von Gierke's disease (glycogenosis type I).

Authors:  R J Havel; E O Balasse; H E Williams; J P Kane; N Segel
Journal:  Trans Assoc Am Physicians       Date:  1969

7.  [Metabolism studies in children and young adults with glycogenoses].

Authors:  I Matschke; J Neubaur; B Willms; H Wolf
Journal:  Monatsschr Kinderheilkd       Date:  1969-04

8.  [Gout as a complication of adult glycogen storage disease].

Authors:  J Neubaur; B Willms; H D Söling; W Creutzfeldt
Journal:  Arch Klin Med       Date:  1969

9.  Studies on dietary correction of metabolic abnormalities in hepatorenal glycogenosis.

Authors:  R C Kelsch; W J Oliver
Journal:  Pediatr Res       Date:  1969-03       Impact factor: 3.756

10.  Hyperlipemia in children with liver glycogen disease.

Authors:  J Fernandes; N A Pikaar
Journal:  Am J Clin Nutr       Date:  1969-05       Impact factor: 7.045
View more
  8 in total

Review 1.  Dietary dilemmas in the management of glycogen storage disease type I.

Authors:  Kaustuv Bhattacharya
Journal:  J Inherit Metab Dis       Date:  2011-04-14       Impact factor: 4.982

2.  The natural history of liver glycogenosis due to phosphorylase kinase deficiency: a longitudinal study of 41 patients.

Authors:  P J Willems; W J Gerver; R Berger; J Fernandes
Journal:  Eur J Pediatr       Date:  1990-01       Impact factor: 3.183

Review 3.  The glycogen storage diseases.

Authors:  B E Ryman
Journal:  J Clin Pathol Suppl (R Coll Pathol)       Date:  1974

4.  Fat-derived fuels during a 24-hour fast in children.

Authors:  J I Wolfsdorf; A Sadeghi-Nejad; B Senior
Journal:  Eur J Pediatr       Date:  1982-03       Impact factor: 3.183

Review 5.  Dietary management in glycogen storage disease type III: what is the evidence?

Authors:  Terry G J Derks; G Peter A Smit
Journal:  J Inherit Metab Dis       Date:  2014-08-28       Impact factor: 4.982

6.  The use of sodium DL-3-Hydroxybutyrate in severe acute neuro-metabolic compromise in patients with inherited ketone body synthetic disorders.

Authors:  Kaustuv Bhattacharya; Walid Matar; Adviye Ayper Tolun; Beena Devanapalli; Sue Thompson; Troy Dalkeith; Kate Lichkus; Michel Tchan
Journal:  Orphanet J Rare Dis       Date:  2020-02-18       Impact factor: 4.123

7.  Liver Glycogen Phosphorylase Deficiency Leads to Profibrogenic Phenotype in a Murine Model of Glycogen Storage Disease Type VI.

Authors:  Lane H Wilson; Jun-Ho Cho; Ana Estrella; Joan A Smyth; Rong Wu; Tayoot Chengsupanimit; Laurie M Brown; David A Weinstein; Young Mok Lee
Journal:  Hepatol Commun       Date:  2019-09-24

8.  Impaired Very-Low-Density Lipoprotein catabolism links hypoglycemia to hypertriglyceridemia in Glycogen Storage Disease type Ia.

Authors:  Joanne A Hoogerland; Fabian Peeks; Brenda S Hijmans; Justina C Wolters; Sander Kooijman; Trijnie Bos; Aycha Bleeker; Theo H van Dijk; Henk Wolters; Albert Gerding; Karen van Eunen; Rick Havinga; Amanda C M Pronk; Patrick C N Rensen; Gilles Mithieux; Fabienne Rajas; Folkert Kuipers; Dirk-Jan Reijngoud; Terry G J Derks; Maaike H Oosterveer
Journal:  J Inherit Metab Dis       Date:  2021-04-07       Impact factor: 4.982
  8 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.