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Literature DB >> 4226289

Hurler's syndrome: biosynthesis of acid mucopolysaccharides in tissue culture.

R Matalon, A Dorfman.

Abstract

Entities: Chemical Disease

Mesh：

Substances：

Year: 1966 PMID： 4226289 PMCID： PMC220063 DOI： 10.1073/pnas.56.4.1310

Source DB: PubMed Journal: Proc Natl Acad Sci U S A ISSN： 0027-8424 Impact factor: 11.205

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26 in total

1. ENZYMATIC DEGRADATION OF CHONDROMUCOPROTEIN.

Authors: J D GREGORY; T C LAURENT; L RODEN
Journal: J Biol Chem Date: 1964-10 Impact factor: 5.157

2. THE BIOSYNTHESIS OF CHONDROITIN SULFATE BY A CELL-FREE PREPARATION.

Authors: R L PERLMAN; A TELSER; A DORFMAN
Journal: J Biol Chem Date: 1964-11 Impact factor: 5.157

3. Determination of 2-deoxy-2-sulfoaminohexose content of mucopolysaccharides.

Authors: D LAGUNOFF; G WARREN
Journal: Arch Biochem Biophys Date: 1962-12 Impact factor: 4.013

4. The molecular weight of sodium chondroitin sulfate by light scattering.

Authors: M B MATHEWS
Journal: Arch Biochem Biophys Date: 1956-04 Impact factor: 4.013

5. Chemistry of beta-heparin (chondroitinsulfuric acid-B).

Authors: J A CIFONELLI; J LUDOWIEG; A DORFMAN
Journal: J Biol Chem Date: 1958-09 Impact factor: 5.157

6. The pathology and chemistry of a case of gargoylism. Appendix. Chemical analysis of tissue polysaccharides.

Authors: S A BARKER; M STACEY
Journal: J Clin Pathol Date: 1956-11 Impact factor: 3.411

7. Method for the determination of hexosamines in tissues.

Authors: N F BOAS
Journal: J Biol Chem Date: 1953-10 Impact factor: 5.157

8. The biosynthesis of chondroitin-sulfate protein complex.

Authors: A Telser; H C Robinson; A Dorfman
Journal: Proc Natl Acad Sci U S A Date: 1965-09 Impact factor: 11.205

9. METABOLISM OF ACID MUCOPOLYSACCHARIDES.

Authors: A DORFMAN
Journal: Biophys J Date: 1964-01 Impact factor: 4.033

10. Chondrogenesis, studied with the electron microscope.

Authors: G C GODMAN; K R PORTER
Journal: J Biophys Biochem Cytol Date: 1960-12

40 in total

1. Kniest syndrome with dominant inheritance and mucopolysacchariduria.

Authors: H J Kim; N G Beratis; P Brill; E Raab; K Hirschhorn; R Matalon
Journal: Am J Hum Genet Date: 1975-11 Impact factor: 11.025

2. The mucopolysaccharidoses.

Authors: C A Pennock; I C Barnes
Journal: J Med Genet Date: 1976-06 Impact factor: 6.318

3. Synthesis of acid mucopolysaccharides by glial tumor cells in tissue culture.

Authors: A Dorfman; P L Ho
Journal: Proc Natl Acad Sci U S A Date: 1970-06 Impact factor: 11.205

4. Synthesis of glycosaminoglycans by human skin fibroblasts cultured on collagen gels.

Authors: J T Gallagher; N Gasiunas; S L Schor
Journal: Biochem J Date: 1980-08-15 Impact factor: 3.857

5. SSIEM Award. Aspartoacylase deficiency: the enzyme defect in Canavan disease.

Authors: R Matalon; R Kaul; J Casanova; K Michals; A Johnson; I Rapin; P Gashkoff; M Deanching
Journal: J Inherit Metab Dis Date: 1989 Impact factor: 4.982

6. The disorder of hyaluronic acid metabolism in cultured skin fibroblasts derived from a patient with the Hurler syndrome.

Authors: R J Germinario; A Kahlenberg; L Pinsky
Journal: Biochem J Date: 1973-03 Impact factor: 3.857

7. The mucopolysaccharidoses: inborn errors of glycosaminoglycan catabolism.

Authors: M Cantz; J Gehler
Journal: Hum Genet Date: 1976-06-29 Impact factor: 4.132

8. Hurler's, Hunter's and Morquio's syndromes. A biochemical study in the light of current views of the underlying defects.

Authors: M F Dean; H Muir; R J Ewins
Journal: Biochem J Date: 1971-08 Impact factor: 3.857

9. Biochemical studies on the sulphated glycosaminoglycan fraction of skin fibroblasts cultured from a patient with the Hurler syndrome.

Authors: R J Germinario; A Kahlenberg; L Pinsky
Journal: Biochem J Date: 1973-03 Impact factor: 3.857

10. The defect in the Hurler and Scheie syndromes: deficiency of -L-iduronidase.

Authors: G Bach; R Friedman; B Weissmann; E F Neufeld
Journal: Proc Natl Acad Sci U S A Date: 1972-08 Impact factor: 11.205