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20 in total

1. Propionyl-CoA-carboxylase determination: study of enzyme parameters in cultured skin fibroblasts from enzyme-deficient and normal subjects.

Authors: P Divry; M O Rolland; N Dingeon; M Mathieu; J Cotte; P Guibaud
Journal: J Inherit Metab Dis Date: 1978 Impact factor: 4.982

2. Isovaleric, methylmalonic, and propionic acid decrease anesthetic EC50 in tadpoles, modulate glycine receptor function, and interact with the lipid 1,2-dipalmitoyl-Sn-glycero-3-phosphocholine.

Authors: Yun Weng; Tienyi Theresa Hsu; Jing Zhao; Stefanie Nishimura; Gerald G Fuller; James M Sonner
Journal: Anesth Analg Date: 2009-05 Impact factor: 5.108

3. Genetic complementation of propionyl-CoA carboxylase deficiency in cultured human fibroblasts.

Authors: R A Gravel; K F Lam; K J Scully; Y Hsia
Journal: Am J Hum Genet Date: 1977-07 Impact factor: 11.025

4. Clinical outcome and long-term management of 17 patients with propionic acidaemia.

Authors: S B van der Meer; F Poggi; M Spada; J P Bonnefont; H Ogier; P Hubert; E Depondt; D Rapoport; D Rabier; C Charpentier; P Parvy; J Bardet; P Kamoun; J M Saudubray
Journal: Eur J Pediatr Date: 1996-03 Impact factor: 3.183

Review 5. Food intolerance in humans.

Authors: R H Herman; L Hagler
Journal: West J Med Date: 1979-02

6. Inherited propionyl-Coa carboxylase deficiency in "ketotic hyperglycinemia".

Authors: Y E Hsia; K J Scully; L E Rosenberg
Journal: J Clin Invest Date: 1971-01 Impact factor: 14.808

Review 7. [Methylmalonic aciduria. Classification, diagnosis and therapy (author's transl)].

Authors: D Leupold
Journal: Klin Wochenschr Date: 1977-01-15

8. 3-hydroxypropionate: significance of -oxidation of propionate in patients with propionic acidemia and methylmalonic acidemia.

Authors: T Ando; K Rasmussen; W L Nyhan; D Hull
Journal: Proc Natl Acad Sci U S A Date: 1972-10 Impact factor: 11.205

9. Absence of cross-reacting material in isolated propionyl CoA carboxylase deficiency: nature of residual carboxylating activity.

Authors: F Kalousek; M D Orsulak; L R Rosenberg
Journal: Am J Hum Genet Date: 1983-05 Impact factor: 11.025

10. Propionicacidemia: absence of alpha-chain mRNA in fibroblasts from patients of the pccA complementation group.

Authors: A M Lamhonwah; R A Gravel
Journal: Am J Hum Genet Date: 1987-12 Impact factor: 11.025