Literature DB >> 4084243

Acidic metabolites of phenylalanine in plasma of phenylketonurics.

M Tuchman, R O Fisch, M L Ramnaraine, W Krivit.   

Abstract

Seven aromatic metabolites of phenylalanine were determined in plasma of 20 patients with classical phenylketonuria by means of capillary gas chromatography. The results obtained showed good correlation with plasma phenylalanine levels. Plasma aromatic acid levels may prove useful in the diagnosis and management of phenylketonuria, as well as in research of this disorder.

Entities:  

Mesh：

Substances：

Year:  1985        PMID： 4084243     DOI： 10.1016/0006-2944(85)90112-7

Source DB:  PubMed          Journal:  Biochem Med        ISSN： 0006-2944


  3 in total

1.  A synopsis of the unconjugated acidic transamination metabolites of phenylalanine in phenylketonuria.

Authors:  U Langenbeck; A Behbehani; A Mench-Hoinowski
Journal:  J Inherit Metab Dis       Date:  1992       Impact factor: 4.982

2.  L-carnitine protects DNA oxidative damage induced by phenylalanine and its keto acid derivatives in neural cells: a possible pathomechanism and adjuvant therapy for brain injury in phenylketonuria.

Authors:  Jéssica Lamberty Faverzani; Aline Steinmetz; Marion Deon; Desirèe Padilha Marchetti; Gilian Guerreiro; Angela Sitta; Daniella de Moura Coelho; Franciele Fatima Lopes; Leopoldo Vinicius Martins Nascimento; Luiza Steffens; Jeferson Gustavo Henn; Matheus Bernardes Ferro; Verônica Bidinotto Brito; Moacir Wajner; Dinara Jaqueline Moura; Carmen Regla Vargas
Journal:  Metab Brain Dis       Date:  2021-07-03       Impact factor: 3.584

3.  Carcinogenic effects in a phenylketonuria mouse model.

Authors:  Neil Sidell; Lijuan Hao; Marzia Pasquali; J David McDonald
Journal:  PLoS One       Date:  2009-01-27       Impact factor: 3.240
  3 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.