Literature DB >> 4045961

Two brothers with Martsolf's syndrome.

J M Sánchez, C Barreiro, H Freilij.   

Abstract

Two brothers affected by a syndrome consisting of short stature, hypogonadism, and severe mental retardation are reported. The syndrome shares the features of that described by Martsolf et al in two brothers born to a consanguineous Polish Jewish couple. Although our patients' parents are Sephardic Jews, they deny consanguinity. These observations and personal knowledge of another affected Jewish boy raise the question of whether Martsolf's syndrome is a new entity that should be included in the group of those that affect mainly Jewish people, and whether its pattern of inheritance is X linked recessive or autosomal recessive limited to males.

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Year:  1985        PMID: 4045961      PMCID: PMC1049456          DOI: 10.1136/jmg.22.4.308

Source DB:  PubMed          Journal:  J Med Genet        ISSN: 0022-2593            Impact factor:   6.318


  1 in total

1.  Severe mental retardation, cataracts, short stature, and primary hypogonadism in two brothers.

Authors:  J T Martsolf; A G Hunter; J C Haworth
Journal:  Am J Med Genet       Date:  1978
  1 in total
  8 in total

1.  Cerebro-oculo-facio-skeletal syndrome with a nucleotide excision-repair defect and a mutated XPD gene, with prenatal diagnosis in a triplet pregnancy.

Authors:  J M Graham ; K Anyane-Yeboa; A Raams; E Appeldoorn; W J Kleijer; V H Garritsen; D Busch; T G Edersheim; N G Jaspers
Journal:  Am J Hum Genet       Date:  2001-07-03       Impact factor: 11.025

2.  Microcephaly, mental retardation, cataracts, and hypogonadism in sibs: Martsolf's syndrome.

Authors:  M G Harbord; M Baraitser; J Wilson
Journal:  J Med Genet       Date:  1989-06       Impact factor: 6.318

3.  Manitoba aboriginal kindred with original cerebro-oculo- facio-skeletal syndrome has a mutation in the Cockayne syndrome group B (CSB) gene.

Authors:  L B Meira; J M Graham; C R Greenberg; D B Busch; A T Doughty; D W Ziffer; D M Coleman; I Savre-Train; E C Friedberg
Journal:  Am J Hum Genet       Date:  2000-03-15       Impact factor: 11.025

4.  Martsolf syndrome in a brother and sister: clinical features and pattern of inheritance.

Authors:  R C Hennekam; A G van de Meeberg; J M van Doorne; P F Dijkstra; J B Bijlsma
Journal:  Eur J Pediatr       Date:  1988-06       Impact factor: 3.183

5.  Martsolf's syndrome in a non-Jewish boy.

Authors:  P Strisciuglio; M Costabile; M Esposito; S Di Maio
Journal:  J Med Genet       Date:  1988-04       Impact factor: 6.318

6.  Novel RAB3GAP1 Mutation in the First Tunisian Family With Warburg Micro Syndrome.

Authors:  Nesrine Kerkeni; Maher Kharrat; Faouzi Maazoul; Hela Boudabous; Ridha M'rad; Mediha Trabelsi
Journal:  J Clin Neurol       Date:  2022-02-14       Impact factor: 3.077

7.  Mutation in Rab3 GTPase-activating protein (RAB3GAP) noncatalytic subunit in a kindred with Martsolf syndrome.

Authors:  Irene A Aligianis; Neil V Morgan; Marina Mione; Colin A Johnson; Elisabeth Rosser; Raoul C Hennekam; Gill Adams; Richard C Trembath; Daniela T Pilz; Neil Stoodley; Anthony T Moore; Steve Wilson; Eamonn R Maher
Journal:  Am J Hum Genet       Date:  2006-02-14       Impact factor: 11.025

Review 8.  Hypogonadotropic hypogonadism due to variants in RAB3GAP2: expanding the phenotypic and genotypic spectrum of Martsolf syndrome.

Authors:  Wanxue Xu; Lacey Plummer; Richard Quinton; Francesca Swords; William F Crowley; Stephanie B Seminara; Ravikumar Balasubramanian
Journal:  Cold Spring Harb Mol Case Stud       Date:  2020-06-12
  8 in total

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