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Literature DB >> 3983062

Fatal splenic rupture in Ehlers-Danlos syndrome.

Abstract

A fatal case of Ehlers-Danlos syndrome (Type IV) is described. Autopsy revealed splenic rupture that had resulted from spontaneous haemorrhage into the splenic parenchyma. This is a previously unrecorded complication of Ehlers-Danlos syndrome and should be considered in the differential diagnosis of chest and abdominal pain in patients with this condition.

Entities: Disease Species

Mesh：

Year: 1985 PMID： 3983062 PMCID： PMC2418189 DOI： 10.1136/pgmj.61.713.259

Source DB: PubMed Journal: Postgrad Med J ISSN： 0032-5473 Impact factor: 2.401

11 in total

1. Ehlers-Danlos syndrome with multiple arterial lesions.

Authors: S Imahori; R M Bannerman; C J Graf; J C Brennan
Journal: Am J Med Date: 1969-12 Impact factor: 4.965

2. Ehlers-Danlos syndrome causing intestinal perforation.

Authors: R T Aldridge
Journal: Br J Surg Date: 1967-01 Impact factor: 6.939

3. Altered secretion of type III procollagen in a form of type IV Ehlers-Danlos syndrome. Biochemical studies in cultured fibroblasts.

Authors: P H Byers; K A Holbrook; G S Barsh; L T Smith; P Bornstein
Journal: Lab Invest Date: 1981-04 Impact factor: 5.662

Review 4. Molecular abnormalities of collagen: a review.

Authors: F M Pope; A C Nicholls; J Dorling; J Webb
Journal: J R Soc Med Date: 1983-12 Impact factor: 5.344

Review 5. Molecular pathology in inherited disorders of collagen metabolism.

Authors: P H Byers; G S Barsh; K A Holbrook
Journal: Hum Pathol Date: 1982-02 Impact factor: 3.466

6. EDS IV (acrogeria): new autosomal dominant and recessive types.

Authors: F M Pope; A C Nicholls; P M Jones; R S Wells; D Lawrence
Journal: J R Soc Med Date: 1980-03 Impact factor: 5.344

7. Ehlers-Danlos syndrome and "congenital" arteriovenous fistulae. A clinicopathologic study of a family.

Authors: H T Lynch; A L Larsen; R Wilson; C L Magnuson
Journal: JAMA Date: 1965-11-29 Impact factor: 56.272

8. Ehlers-Danlos syndrome.

Authors: R M Bannerman; C J Graf; J F Upson
Journal: Br Med J Date: 1967-08-26

9. Pregnancy complications in type IV Ehlers-Danlos Syndrome.

Authors: N L Rudd; C Nimrod; K A Holbrook; P H Byers
Journal: Lancet Date: 1983-01-01 Impact factor: 79.321

10. Patients with Ehlers-Danlos syndrome type IV lack type III collagen.

Authors: F M Pope; G R Martin; J R Lichtenstein; R Penttinen; B Gerson; D W Rowe; V A McKusick
Journal: Proc Natl Acad Sci U S A Date: 1975-04 Impact factor: 11.205

7 in total

Review 1. Spontaneous common iliac arteries rupture in Ehlers-Danlos syndrome type IV: report of two cases and review of the literature.

Authors: K Habib; M A Memon; D A Reid; B J Fairbrother
Journal: Ann R Coll Surg Engl Date: 2001-03 Impact factor: 1.891

Review 2. Visceroptosis of the bowel in the hypermobility type of Ehlers-Danlos syndrome: presentation of a rare manifestation and review of the literature.

Authors: Eyal Reinstein; Mark Pimentel; Mitchel Pariani; Stephen Nemec; Thomas Sokol; David L Rimoin
Journal: Eur J Med Genet Date: 2012-07-07 Impact factor: 2.708

Review 7. Ehlers-Danlos syndrome type IV.

Authors: Dominique P Germain
Journal: Orphanet J Rare Dis Date: 2007-07-19 Impact factor: 4.123