Literature DB >> 3921377

An infant with Marfanoid phenotype and congenital contractures associated with ocular and cardiovascular anomalies, cerebral white matter hypoplasia and spinal axonopathy.

P Tamminga, F G Jennekens, P G Barth, P Fleury, H van den Berg, J W Oorthuys.   

Abstract

An infant is presented with a Marfanoid phenotype and congenital contractures. In addition to this she showed severe neurological and ocular abnormalities. Cardiac insufficiency due to mitral and tricuspidal valve prolapse caused her death at the age of 6 months. Postmortem examination showed axonal pathology of the anterior horns and roots of the spinal cord, and white matter hypoplasia of the brain.

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Year:  1985        PMID: 3921377     DOI: 10.1007/bf00442148

Source DB:  PubMed          Journal:  Eur J Pediatr        ISSN: 0340-6199            Impact factor:   3.183


  11 in total

1.  "New" syndrome of congenital contractural arachnodactyly originally described by Marfan in 1896.

Authors:  F Hecht; R K Beals
Journal:  Pediatrics       Date:  1972-04       Impact factor: 7.124

2.  Congenital contractural arachnodactyly and intraocular colobomas.

Authors:  L A Bard
Journal:  Birth Defects Orig Artic Ser       Date:  1979

3.  Multisystem neuronal degeneration, hepatosplenomegaly, and adrenocortical deficiency associated with reduced tissue arachidonic acid.

Authors:  P J Dyck; J K Yao; D E Knickerbocker; R T Holman; M R Gomez; A B Hayles; E H Lambert
Journal:  Neurology       Date:  1981-08       Impact factor: 9.910

4.  Early cardiac manifestations of Marfan's syndrome in the newborn.

Authors:  Z Lababidi; C Monzon
Journal:  Am Heart J       Date:  1981-11       Impact factor: 4.749

5.  Marfan syndrome with contractural arachnodactyly and severe mitral regurgitation in a premature infant.

Authors:  M A Gruber; T P Graham; E Engel; C Smith
Journal:  J Pediatr       Date:  1978-07       Impact factor: 4.406

6.  Hypoplasia of hemispheric white matter, peculiar pallidal changes and dysplastic inferior olives in a child with psychomotor retardation.

Authors:  D S Horoupian; M Dal Canto; I Rapin
Journal:  Acta Neuropathol       Date:  1978-06-30       Impact factor: 17.088

7.  [Congenital contractural arachnodactyly (CCA syndrome)--an autosomal dominant hereditary connective tissue disease].

Authors:  P Meinecke; E Schaefer; E Passarge
Journal:  Klin Padiatr       Date:  1983 Jan-Feb       Impact factor: 1.349

8.  Cerebral white-matter hypoplasia.

Authors:  A S Chattha; E P Richardson
Journal:  Arch Neurol       Date:  1977-03

9.  Infantile neuroaxonal dystrophy.

Authors:  J Aicardi; P Castelein
Journal:  Brain       Date:  1979-12       Impact factor: 13.501

Review 10.  The distal arthrogryposes: delineation of new entities--review and nosologic discussion.

Authors:  J G Hall; S D Reed; G Greene
Journal:  Am J Med Genet       Date:  1982-02
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  4 in total

1.  Megalocornea. Clinical and genetic aspects.

Authors:  F M Meire
Journal:  Doc Ophthalmol       Date:  1994       Impact factor: 2.379

2.  Dilated neonatal cisterna magna and Marfan syndrome.

Authors:  Vimal Vasu; Anne H Child; Neena Modi; Mary Rutherford; Frances Cowan
Journal:  BMJ Case Rep       Date:  2011-07-28

3.  Neonatal Marfan syndrome with congenital arachnodactyly, flexion contractures, and severe cardiac valve insufficiency.

Authors:  I M Buntinx; P J Willems; S E Spitaels; P J Van Reempst; A M De Paepe; J E Dumon
Journal:  J Med Genet       Date:  1991-04       Impact factor: 6.318

4.  Recurrent ctb(7)(q31.3) and possible laminin involvement in a neonatal cutis laxa with a Marfan phenotype.

Authors:  D Bonneau; J L Huret; G Godeau; D Couet; M Putterman; J Tanzer; P Babin; M Larrègue
Journal:  Hum Genet       Date:  1991-07       Impact factor: 4.132

  4 in total

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