[Congenital spontaneously ruptured epidermoid cyst of the iris].

At the age of 8 months a healthy boy developed a epidermoid cyst of the iris which increased rapidly in size and ruptured when he was 12 months old. Because of the clinically suspected diagnosis of medulla epithelioma an en-bloc excision was performed. The tumor consisted of keratinizing squamous epithelium producing masses of keratin. After an unremarkable postoperative course lasting four months, the boy developed an immunologic reaction to the tectonic graft in association with Coats' disease six months after the operation.