Literature DB >> 3721321

Plasma exchange for acute cholestasis in homozygous sickle cell disease.

E Svarch, A González, R Villaescusa, P Basanta.   

Abstract

A child with sickle cell disease presented acute chest syndrome, acute cholestasis and a neurological syndrome. Bilirubin, LDH, alkaline phosphatase, urea and creatinines were markedly increased. Circulating immune complexes were slightly elevated. The patient improved dramatically after a plasma exchange.

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Year:  1986        PMID: 3721321

Source DB:  PubMed          Journal:  Haematologia (Budap)        ISSN: 0017-6559


  4 in total

1.  Case of fatal sickle cell intrahepatic cholestasis despite use of exchange transfusion in an African-American patient.

Authors:  Daniel B Costa; Rebecca A Miksad; Michael S Buff; Yihong Wang; Bruce J Dezube
Journal:  J Natl Med Assoc       Date:  2006-07       Impact factor: 1.798

Review 2.  Acute liver function decompensation in a patient with sickle cell disease managed with exchange transfusion and endoscopic retrograde cholangiography.

Authors:  Haris Papafragkakis; Mel A Ona; Kinesh Changela; Swayamprabha Sadanandan; Abraham Jelin; Sury Anand; Sushil Duddempudi
Journal:  Therap Adv Gastroenterol       Date:  2014-09       Impact factor: 4.409

3.  Intrahepatic cholestasis in sickle cell disease: a case report.

Authors:  Denise Menezes Brunetta; Ana Cristina Silva-Pinto; Maria do Carmo Favarin de Macedo; Sarah Cristina Bassi; Joao Victor Piccolo Feliciano; Fernanda Borges Ribeiro; Benedito de Pina Almeida Prado; Gil Cunha De Santis; Ivan de Lucena Angulo; Dimas Tadeu Covas
Journal:  Anemia       Date:  2010-12-21

4.  Rare but Lethal Hepatopathy-Sickle Cell Intrahepatic Cholestasis and Management Strategies.

Authors:  Aamir Malik; Chandni Merchant; Mana Rao; Rosemary P Fiore
Journal:  Am J Case Rep       Date:  2015-11-28
  4 in total

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