Literature DB >> 3688102

Spatial and temporal sequence of corneal crystal deposition in nephropathic cystinosis.

R B Melles1, J A Schneider, N A Rao, B Katz.   

Abstract

We studied 15 patients with infantile nephropathic cystinosis. We found that anterior corneal cystine crystal deposition began early in life and proceeded posteriorly as the patient aged; deposition advanced more rapidly in the periphery. Ultrastructural analysis of a corneal button obtained from a 20-year-old patient undergoing corneal transplantation confirmed our clinical observations that crystals were deposited throughout the entire central stroma.

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Year:  1987        PMID： 3688102     DOI： 10.1016/0002-9394(87)90171-1

Source DB:  PubMed          Journal:  Am J Ophthalmol        ISSN： 0002-9394            Impact factor:   5.258


  8 in total

1.  [Unclear, bilateral retinal dystrophy. 35-year old female patient with glare sensation].

Authors:  G Rössler; S Roters; M Severin; G K Krieglstein
Journal:  Ophthalmologe       Date:  2003-11       Impact factor: 1.059

2.  Clearance of corneal crystals in nephropathic cystinosis by topical cysteamine 0.5%.

Authors:  N P Jones; R J Postlethwaite; J L Noble
Journal:  Br J Ophthalmol       Date:  1991-05       Impact factor: 4.638

Review 3.  Ophthalmic manifestations and histopathology of infantile nephropathic cystinosis: report of a case and review of the literature.

Authors:  Ekaterini Tsilou; Min Zhou; William Gahl; Pamela C Sieving; Chi-Chao Chan
Journal:  Surv Ophthalmol       Date:  2007 Jan-Feb       Impact factor: 6.048

Review 4.  Update on nephropathic cystinosis.

Authors:  J A Schneider; B Katz; R B Melles
Journal:  Pediatr Nephrol       Date:  1990-11       Impact factor: 3.714

5.  Early-onset chronic renal failure as a presentation of infantile nephropathic cystinosis.

Authors:  W G van't Hoff; S E Ledermann; M Waldron; R S Trompeter
Journal:  Pediatr Nephrol       Date:  1995-08       Impact factor: 3.714

6.  Corneal thickness in nephropathic cystinosis.

Authors:  B Katz; R B Melles; J A Schneider; N A Rao
Journal:  Br J Ophthalmol       Date:  1989-08       Impact factor: 4.638

7.  Quantitative in vivo and ex vivo confocal microscopy analysis of corneal cystine crystals in the Ctns knockout mouse.

Authors:  Jennifer Simpson; Chyong Jy Nien; Kevin Flynn; Brian Jester; Stephanie Cherqui; James Jester
Journal:  Mol Vis       Date:  2011-08-17       Impact factor: 2.367

8.  A case of corneal cystinosis in a patient with rickets and chronic renal failure.

Authors:  Jae Yon Won; Hyung Bin Hwang; Sung Kun Chung
Journal:  Indian J Ophthalmol       Date:  2015-10       Impact factor: 1.848
  8 in total

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