| Literature DB >> 36006424 |
Dario Didona1, Julia Hinterseher2, Rüdiger Eming2,3.
Abstract
Autoimmune bullous diseases (AIBD) comprise a group of organ-specific autoimmune diseases which are characterised by the production of autoantibodies against adhesion molecules and structural proteins of skin and mucosae. Depending on the target protein, AIBD are classified into intraepidermal (pemphigus group) and subepidermal (pemphigoid group, epidermolysis bullosa acquisita, dermatitis herpetiformis) blistering disorders. Depending on the clinical entity, patients can develop blisters, pustules, erosions, and erythema on the skin and mucosae.Entities:
Keywords: Autoantibodies; Blistering skin diseases; Pemphigoid; Pemphigus; Rare skin diseases
Mesh:
Year: 2022 PMID: 36006424 DOI: 10.1007/s00105-022-05036-y
Source DB: PubMed Journal: Dermatologie (Heidelb) ISSN: 2731-7005