Literature DB >> 3597897

Congenital bronchiectasis due to cartilage deficiency: CT demonstration.

Y Watanabe, Y Nishiyama, H Kanayama, K Enomoto, K Kato, M Takeichi.   

Abstract

The CT appearance of bronchiectasis on inspiration and expiration in a patient with congenital bronchiectasis due to cartilage deficiency (Williams-Campbell syndrome) is reported. Computed tomography demonstrated characteristic findings of this syndrome, ballooning of bronchi on inspiration and collapse on expiration.

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Mesh:

Year:  1987        PMID: 3597897

Source DB:  PubMed          Journal:  J Comput Assist Tomogr        ISSN: 0363-8715            Impact factor:   1.826


  5 in total

1.  Williams-Campbell syndrome presenting in an adult.

Authors:  Quentin Christopher Jones; Christopher G Wathen
Journal:  BMJ Case Rep       Date:  2012-09-18

2.  Lung transplantation for Williams-Campbell syndrome with a probable familial association.

Authors:  S Rodrigo Burguete; Stephanie M Levine; Marcos I Restrepo; Luis F Angel; Deborah J Levine; Jacqueline J Coalson; Jay I Peters
Journal:  Respir Care       Date:  2012-02-17       Impact factor: 2.258

3.  Williams-Campbell syndrome: a case report.

Authors:  Maria Konoglou; Konstantinos Porpodis; Paul Zarogoulidis; Nikolaos Loridas; Nikolaos Katsikogiannis; Alexandros Mitrakas; Vasilis Zervas; Theodoros Kontakiotis; Despoina Papakosta; Panagiotis Boglou; Stamatia Bakali; Nikolaos Courcoutsakis; Konstantinos Zarogoulidis
Journal:  Int J Gen Med       Date:  2012-01-11

Review 4.  The clinical manifestations, diagnosis and management of williams-campbell syndrome.

Authors:  Adrian Pedro Noriega Aldave; DO William Saliski
Journal:  N Am J Med Sci       Date:  2014-09

5.  Williams-Campbell syndrome: an unusual presentation in an adult patient.

Authors:  Mili Rohilla; Carlos Previgliano; Atefeh Geimadi; Guillermo Sangster
Journal:  BJR Case Rep       Date:  2020-11-02
  5 in total

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