| Literature DB >> 35948828 |
Leanne H Q Chin1, Kevin K F Fung2, Joyce P K Chan2, Amanda N C Kan3, M K Yuen2.
Abstract
Kaposiform haemangioendothelioma (KHE) is a rare childhood disease classified by the International Society for the Study of Vascular Anomalies (ISSVA) as a locally aggressive vascular tumor. It has been reported to affect any site, with a predilection for the extremities and trunk. Although it typically manifests as an enlarging cutaneous or soft tissue lesion, less than 10% of cases have no skin involvement, with the retroperitoneum being the most frequently involved extracutaneous site. Approximately twenty cases of KHE with bony involvement have been reported in the literature to date, with only five of those cases involving the spine specifically.We present a, rare case of KHE who presented with progressive fixed hyperlordotic deformity, multiple non-specific spinal lesions, and abnormal blood tests, posing a clinical and radiological diagnostic challenge. Additionally, we conducted a thorough review of the literature to compare and contrast the various multimodality imaging manifestations of KHE involving the spine.Entities:
Keywords: Kaposiform haemangioendothelioma (KHE); Kasabach-Merritt syndrome (KMS); Spine
Year: 2022 PMID: 35948828 DOI: 10.1007/s00256-022-04152-z
Source DB: PubMed Journal: Skeletal Radiol ISSN: 0364-2348 Impact factor: 2.128