Literature DB >> 35868678

Biliary Atresia in Children: Update on Disease Mechanism, Therapies, and Patient Outcomes.

Swati Antala1, Sarah A Taylor2.   

Abstract

Biliary atresia is a rare disease but remains the most common indication for pediatric liver transplantation as there are no effective medical therapies to slow progression after diagnosis. Variable contribution of genetic, immune, and environmental factors contributes to disease heterogeneity among patients with biliary atresia. Developing a deeper understanding of the disease mechanism will help to develop targeted medical therapies and improve patient outcomes.
Copyright © 2022 Elsevier Inc. All rights reserved.

Entities:  

Keywords:  Biliary atresia; Neonatal cholestasis; Pediatric liver transplantation; Transplant outcomes

Mesh：

Year:  2022        PMID： 35868678      PMCID： PMC9309872          DOI： 10.1016/j.cld.2022.03.001

Source DB:  PubMed          Journal:  Clin Liver Dis        ISSN： 1089-3261            Impact factor:   6.265


  94 in total

1.  Urinary sulfated bile acid concentrations in infants with biliary atresia and breast-feeding jaundice.

Authors:  Toshihiro Muraji; Tokuzo Harada; Kazunori Miki; Takanobu Moriuchi; Masayuki Obatake; Chikara Tsugawa
Journal:  Pediatr Int       Date:  2003-06       Impact factor: 1.524

Review 2.  Prophylactic Antibiotics for Prevention of Cholangitis in Patients With Biliary Atresia Status Post-Kasai Portoenterostomy: A Systematic Review.

Authors:  Katawaetee Decharun; Charles M Leys; Karen W West; S Maria E Finnell
Journal:  Clin Pediatr (Phila)       Date:  2015-07-15       Impact factor: 1.168

3.  A multicenter study of the outcome of biliary atresia in the United States, 1997 to 2000.

Authors:  Benjamin L Shneider; Morton B Brown; Barbara Haber; Peter F Whitington; Kathleen Schwarz; Robert Squires; Jorge Bezerra; Ross Shepherd; Philip Rosenthal; Jay H Hoofnagle; Ronald J Sokol
Journal:  J Pediatr       Date:  2006-04       Impact factor: 4.406

4.  The dendritic cell-T helper 17-macrophage axis controls cholangiocyte injury and disease progression in murine and human biliary atresia.

Authors:  Celine S Lages; Julia Simmons; Avery Maddox; Keaton Jones; Rebekah Karns; Rachel Sheridan; Shiva Kumar Shanmukhappa; Sujit Mohanty; Matthew Kofron; Pierre Russo; Yui-Hsi Wang; Claire Chougnet; Alexander G Miethke
Journal:  Hepatology       Date:  2016-11-10       Impact factor: 17.425

5.  Granulocyte-colony stimulating factor GCSF mobilizes hematopoietic stem cells in Kasai patients with biliary atresia in a phase 1 study and improves short term outcome.

Authors:  AiXuan Holterman; Hoa Pham Anh Nguyen; Evan Nadler; Giap H Vu; Parvathi Mohan; Megan Vu; Thuy Thi Trinh; Huong Thuy Thi Bui; Binh Thanh Nguyen; Anh Tran Quynh; Hien Duy Pham
Journal:  J Pediatr Surg       Date:  2021-04-09       Impact factor: 2.545

6.  Clinical Consequences of Cardiomyopathy in Children With Biliary Atresia Requiring Liver Transplantation.

Authors:  Noelle M Gorgis; Curtis Kennedy; Fong Lam; Kathleen Thompson; Jorge Coss-Bu; Ayse Akcan Arikan; Trung Nguyen; Kathleen Hosek; Tamir Miloh; Saul J Karpen; Daniel J Penny; John Goss; Moreshwar S Desai
Journal:  Hepatology       Date:  2019-02-17       Impact factor: 17.425

7.  Identification of Polycystic Kidney Disease 1 Like 1 Gene Variants in Children With Biliary Atresia Splenic Malformation Syndrome.

Authors:  John-Paul Berauer; Anya I Mezina; David T Okou; Aniko Sabo; Donna M Muzny; Richard A Gibbs; Madhuri R Hegde; Pankaj Chopra; David J Cutler; David H Perlmutter; Laura N Bull; Richard J Thompson; Kathleen M Loomes; Nancy B Spinner; Ramakrishnan Rajagopalan; Stephen L Guthery; Barry Moore; Mark Yandell; Sanjiv Harpavat; John C Magee; Binita M Kamath; Jean P Molleston; Jorge A Bezerra; Karen F Murray; Estella M Alonso; Philip Rosenthal; Robert H Squires; Kasper S Wang; Milton J Finegold; Pierre Russo; Averell H Sherker; Ronald J Sokol; Saul J Karpen
Journal:  Hepatology       Date:  2019-03-21       Impact factor: 17.425

8.  Gamma-glutamyl transferase in the diagnosis of biliary atresia.

Authors:  Kuo-Shu Tang; Li-Tung Huang; Ying-Hsien Huang; Chi-Yin Lai; Chi-Hung Wu; Sheng-Ming Wang; Kao-Pin Hwang; Fu-Chen Huang; Mao-Meng Tiao
Journal:  Acta Paediatr Taiwan       Date:  2007 Jul-Aug

9.  Oligoclonal immunoglobulin repertoire in biliary remnants of biliary atresia.

Authors:  Sarah A Taylor; Padmini Malladi; Xiaomin Pan; Joshua B Wechsler; Kathryn E Hulse; Harris Perlman; Peter F Whitington
Journal:  Sci Rep       Date:  2019-03-14       Impact factor: 4.379

10.  Development and validation of bile acid profile-based scoring system for identification of biliary atresia: a prospective study.

Authors:  Dongying Zhao; Kejun Zhou; Yan Chen; Wei Xie; Yongjun Zhang
Journal:  BMC Pediatr       Date:  2020-05-27       Impact factor: 2.125
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