| Literature DB >> 35790695 |
Fu-Shiuan Whitney Lee1, Chih-Ying Lee1,2, Giun-Yi Hung1,2, Min-Hua Tseng3, Hsin-Hui Wang1, Hsiu-Ju Yen4,5.
Abstract
Complement-mediated hemolytic uremic syndrome (CM-HUS) following chemotherapy for pediatric acute lymphoid neoplasms has rarely been reported. We report the case of an 8-year-old boy with T-lymphoblastic lymphoma (T-LBL) who developed CM-HUS with complement factor H (CFH) mutations (S1191L, V1197A) during induction therapy. Safe administration of chemotherapy after CM-HUS recovery was challenging. By closely monitoring hemolytic and renal parameters during the 2-year treatment period, we observed four episodes of microangiopathic hemolytic anemia (MAHA) with hypocomplementemia and low haptoglobin but no renal dysfunction or thrombocytopenia. Here, we describe the MAHA and CM-HUS episodes in the hopes of elucidating the complex pathophysiology of disorders associated with CFH mutation.Entities:
Keywords: 6-mercaptopurine; Atypical hemolytic uremic syndrome; Complement-mediated hemolytic uremic syndrome; Lymphoblastic lymphoma; Microangiopathic hemolytic anemia
Year: 2022 PMID: 35790695 DOI: 10.1007/s12185-022-03409-6
Source DB: PubMed Journal: Int J Hematol ISSN: 0925-5710 Impact factor: 2.319