Adrenal hemangioblastoma in Von Hippel-Lindau disease as a cause of secondary erythrocytosis.

Von Hippel-Lindau disease (VHLD) is an inherited disorder with protean manifestations including tumors that may cause secondary erythrocytosis: cerebellar hemangioblastoma, renal cell carcinoma, and pheochromocytoma. The case of a woman with VHLD whose secondary erythrocytosis resolved after removal of an adrenal hemangioblastoma is reported. This is the first reported case of adrenal hemangioblastoma in VHLD. Furthermore, it appears that adrenal hemangioblastoma is a cause of secondary erythrocytosis.