Taleaa Masroor1, Ava Ganson Chappell2, Farooq Shahzad2. 1. Aga Khan University, Karachi, Pakistan. 2. Lurie Children's Hospital, Northwestern University Feinberg School of Medicine, Chicago, IL.
Abstract
Background: Osteogenesis imperfecta (OI) is a rare metabolic bone disorder in which collagen production is impaired. Patients have brittle bones that are prone to fracture with minor trauma. Whereas most of the fractures occur in the spine and extremities, fractures of the craniofacial bones are less common. Methods: This report describes the management of a 14-year-old boy with OI type 1 who sustained mandible fractures from an assault. Management consisted of open reduction and internal fixation of the parasymphyseal and angle fractures and closed reduction and mandibulomaxillary fixation of the subcondylar fracture. Results: Surgery resulted in return of premorbid occlusion and good jaw function. Removal of plates and screws was performed 10 months later without incident. Conclusions: This case report discusses the unique anesthetic, surgical, and postoperative considerations for managing mandible fractures in patients with OI.
Background: Osteogenesis imperfecta (OI) is a rare metabolic bone disorder in which collagen production is impaired. Patients have brittle bones that are prone to fracture with minor trauma. Whereas most of the fractures occur in the spine and extremities, fractures of the craniofacial bones are less common. Methods: This report describes the management of a 14-year-old boy with OI type 1 who sustained mandible fractures from an assault. Management consisted of open reduction and internal fixation of the parasymphyseal and angle fractures and closed reduction and mandibulomaxillary fixation of the subcondylar fracture. Results: Surgery resulted in return of premorbid occlusion and good jaw function. Removal of plates and screws was performed 10 months later without incident. Conclusions: This case report discusses the unique anesthetic, surgical, and postoperative considerations for managing mandible fractures in patients with OI.