Literature DB >> 35573561

A Case Report of Behcet's Disease With Thromboses in the Superior Vena Cava and External Iliac Vein.

Faiza Zafar Sayeed1, Muhammad Nashit1, Shaheen Bhatty1, Bushra Z Sayeed1, Fariha Asad1.   

Abstract

Behcet's disease (BD), also known as Behcet's syndrome, is a rare, chronic, autoimmune disorder of unknown origin. Its manifestations are thought to be caused by vasculitis, resulting in damage to blood vessels of all sizes throughout the body. We report a 25-year-old Pakistani male who is sexually active and presents with a one-year history of shortness of breath, cough, exertional dyspnea, and neck and facial swelling. On examination, he had severe anemia, mouth ulcers, distended neck and chest veins, prominent abdominal veins, and a scrotal ulcer. After going through mandatory investigations to evaluate the presenting signs and symptoms, thromboses were found in the major veins, including the superior vena cava (SVC) and external iliac vein, as well as a positive pathergy test. Accordingly, a diagnosis of Behcet's disease with cardiomyopathy and venous thrombosis was made. He was treated with anticoagulants, steroids, and azathioprine for six months and subsequently went into remission.
Copyright © 2022, Sayeed et al.

Entities:  

Keywords:  autoimmune disease; behcet's disease; behcet's syndrome; cardiovascular disease; mucocutaneous ulcers; pathergy; superior vena cava (svc) syndrome; thromboembolic disease; thrombotic angiopathy

Year:  2022        PMID: 35573561      PMCID: PMC9097467          DOI: 10.7759/cureus.24064

Source DB:  PubMed          Journal:  Cureus        ISSN: 2168-8184


  10 in total

1.  A fatal case of Behçet's disease associated with multiple cardiovascular lesions.

Authors:  A Roguin; Y Edoute; S Milo; S Shtiwi; W Markiewicz; S A Reisner
Journal:  Int J Cardiol       Date:  1997-05-23       Impact factor: 4.164

Review 2.  Behçet syndrome: a contemporary view.

Authors:  Hasan Yazici; Emire Seyahi; Gulen Hatemi; Yusuf Yazici
Journal:  Nat Rev Rheumatol       Date:  2018-01-03       Impact factor: 20.543

3.  Vascular involvement in Behçet's syndrome: a retrospective analysis of associations and the time course.

Authors:  Koray Tascilar; Melike Melikoglu; Serdal Ugurlu; Necdet Sut; Erkan Caglar; Hasan Yazici
Journal:  Rheumatology (Oxford)       Date:  2014-06-06       Impact factor: 7.580

4.  Clinical characteristics and radiographic outcomes of vascular Behçet's disease involving the aorta or its major branches.

Authors:  Seulkee Lee; Seonyoung Kang; Yeonghee Eun; Hyungjin Kim; Jaejoon Lee; Eun-Mi Koh; Duk-Kyung Kim; Hoon-Suk Cha
Journal:  Clin Rheumatol       Date:  2022-02-07       Impact factor: 2.980

5.  Major vascular involvement in Behçet's disease: a retrospective study of 796 patients.

Authors:  Yunyun Fei; Xuemei Li; Sen Lin; Xiaojun Song; Qingjun Wu; Yanlin Zhu; Xin Gao; Wen Zhang; Yan Zhao; Xiaofeng Zeng; Fengchun Zhang
Journal:  Clin Rheumatol       Date:  2013-02-27       Impact factor: 2.980

6.  Recurrent Iliofemoral Venous Thrombosis in the Setting of May-Thurner Syndrome as the Presenting Symptom of Behcet's Disease.

Authors:  Sameer Lakha; Chien Yi Maximilian Png; Kevin Chun; Windsor Ting
Journal:  Ann Vasc Surg       Date:  2018-02-23       Impact factor: 1.466

7.  Behçet's disease; A rare refractory patient with vena cava superior syndrome treated with infliximab: a case report and review of the literature.

Authors:  Oguz Abdullah Uyaroglu; Abdulsamet Erden; Levent Kilic; Bora Peynircioğlu; Omer Karadag; Umut Kalyoncu
Journal:  Acta Clin Belg       Date:  2018-09-17       Impact factor: 1.264

8.  Clinical characteristics and risk factors of intestinal involvement in Behçet's syndrome patients: a cross-sectional study from a single center.

Authors:  Cheng-Cheng Hou; Jing-Fen Ye; Hai-Fen Ma; Jian-Long Guan
Journal:  Orphanet J Rare Dis       Date:  2021-03-17       Impact factor: 4.123

9.  Coronavirus disease 2019 in patients with Behcet's disease: a report of 59 cases in Iran.

Authors:  Farhad Shahram; Kamal Esalatmanesh; Alireza Khabbazi; Zahra Rezaieyazdi; Zahra Mirfeizi; Alireza Sadeghi; Mohsen Soroosh; Hoda Kavosi; Majid Alikhani; Shayan Mostafaei
Journal:  Clin Rheumatol       Date:  2021-11-29       Impact factor: 3.650

Review 10.  Pulmonary artery thrombosis as the first presentation of Behçet's syndrome: a case report and review of the literature.

Authors:  Ziyad Alakkas; Waad Kazi; Mohamed Mattar; Eman Abdul Wahhab Salem; Naglaa Fawzy Seleem
Journal:  J Med Case Rep       Date:  2021-06-22
  10 in total

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