| Literature DB >> 35535111 |
Chinmayee Panigrahi1, Hemanta K Nayak2, Susama Patra1, Suvradeep Mitra1.
Abstract
Follicular dendritic cell (FDC) sarcoma is an uncommon tumor of the liver with only 30 previous cases reported in the English literature. Histopathological examination is the gold standard for the diagnosis of FDC sarcoma although the diagnosis is often missed because of its rarity. It usually presents with spindle-cell morphology although epithelioid/biphasic morphology is also well-known. This morphological variation can also pose a diagnostic challenge. We discuss a case of unresectable hepatic FDC sarcoma in an adult male who was diagnosed in core biopsy. We highlight the relevant histomorphological differentials and diagnostic approaches to FDC sarcoma in this anecdote.Entities:
Keywords: AFP, alpha-fetoprotein; CT, computed tomography; E-GIST, epithelioid gastrointestinal stromal tumor; E-LMS, epithelioid leiomyosarcoma; E-MPNST, epithelioid malignant peripheral nerve sheath tumor; EBV, Epstein–Barr virus; EHE, epithelioid hemangioendothelioma; FDC, follicular dendritic cell; HAML, hepatic angiomyolipoma; HCC, hepatocellular carcinoma; IPT, inflammatory pseudotumor; LMP, latent membrane protein; USG, ultrasonography; epithelioid; extranodal; follicular dendritic cell sarcoma; histopathology; liver
Year: 2021 PMID： 35535111 PMCID： PMC9077179 DOI： 10.1016/j.jceh.2021.06.014
Source DB: PubMed Journal: J Clin Exp Hepatol ISSN： 0973-6883