| Literature DB >> 35420313 |
Arash Salamat1, Sebastian Strieth.
Abstract
Cogan I syndrome is a rare disease consisting of vestibulocochlear symptoms and non-syphilitic interstitial keratitis. Although this disease was first described in 1945, its pathogenesis is still unknown. An autoimmune vasculitis etiology is currently discussed. Atypical manifestations are characterized by delayed ocular symptoms or variability of inflammatory eye symptoms. Physical examination often reveals bilateral sensorineural hearing loss. Intratympanic corticosteroid application can be successful.Entities:
Keywords: Autoimmune diseases; Corticosteroids; Deafness; Keratitis; Vasculitis
Mesh:
Year: 2022 PMID: 35420313 DOI: 10.1007/s00106-022-01168-8
Source DB: PubMed Journal: HNO ISSN: 0017-6192 Impact factor: 1.284