Literature DB >> 35401959

Paediatric cholestatic liver disorders for the adult gastroenterologist: a practical guide.

Claire Kelly1, Jeremy Shanika Nayagam1, Stamatina Vogli1, Marianne Samyn1, Deepak Joshi1.   

Abstract

With improvements in the outcomes for cholestatic liver diseases that present in childhood, increasing numbers of patients will require ongoing care as adults. The recent advances in management options coupled with the fact that each adult physician will have a limited number of patients with these conditions means there is a need for those in adult services to develop expertise in these conditions that were historically the domain of paediatrics. This review provides an overview of the most common paediatric cholestatic liver diseases and outlines the clinical manifestations and potential complications, and identifies key management issues unique to each condition for effective ongoing care of these patients. © Author(s) (or their employer(s)) 2021. No commercial re-use. See rights and permissions. Published by BMJ.

Entities:  

Keywords:  cholestasis; cholestatic liver diseases; paediatric liver disease

Year:  2020        PMID: 35401959      PMCID: PMC8989003          DOI: 10.1136/flgastro-2020-101554

Source DB:  PubMed          Journal:  Frontline Gastroenterol        ISSN: 2041-4137


  57 in total

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Journal:  Hepatology       Date:  2019-03-21       Impact factor: 17.425

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  1 in total

1.  Nasobiliary drainage: an effective treatment for pruritus in cholestatic liver disease.

Authors:  Wafaa Ahmed; Rebecca Jeyaraj; David Reffitt; John Devlin; Abid Suddle; John Hunt; Michael A Heneghan; Phillip Harrison; Deepak Joshi
Journal:  Frontline Gastroenterol       Date:  2022-01-11
  1 in total

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